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Creutzfeldt-Jakob Disease Presenting as Nonconvulsive Status Epilepticus
Joint Authors
Haldre, Sulev
Rakitin, Aleksei
Veikat, Vaiko
Õunapuu, Anne
Liigant, Aive
Vibo, R.
Source
Case Reports in Neurological Medicine
Issue
Vol. 2018, Issue 2018 (31 Dec. 2018), pp.1-4, 4 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2018-11-04
Country of Publication
Egypt
No. of Pages
4
Main Subjects
Abstract EN
Creutzfeldt-Jakob disease is a rare, rapidly progressive spongiform encephalopathy in humans.
EEG plays an important role in diagnosing this disease.
In some patients, epileptic activity and encephalopathy from various aetiologies may share morphological features on EEG.
This similarity could create difficulties in EEG interpretation, especially if the patient presents with disturbed consciousness.
In this case report, a 74-year-old female with Creutzfeldt-Jakob disease presented initially with rapidly progressive impairment of consciousness and focal epileptiform activity on EEG.
An EEG performed 25 days later showed periodic sharp-wave complexes with triphasic morphology at a rate of 0.5 Hz, compatible with a diagnosis of Creutzfeldt-Jakob disease.
Based on these results, we recommend that a diagnosis of Creutzfeldt-Jakob disease be considered in patients presenting with a rapid deterioration of consciousness and a clinical presentation of nonconvulsive status epilepticus.
Monitoring these patients with serial EEGs could be useful to establish an accurate diagnosis.
American Psychological Association (APA)
Rakitin, Aleksei& Vibo, R.& Veikat, Vaiko& Õunapuu, Anne& Liigant, Aive& Haldre, Sulev. 2018. Creutzfeldt-Jakob Disease Presenting as Nonconvulsive Status Epilepticus. Case Reports in Neurological Medicine،Vol. 2018, no. 2018, pp.1-4.
https://search.emarefa.net/detail/BIM-1145376
Modern Language Association (MLA)
Rakitin, Aleksei…[et al.]. Creutzfeldt-Jakob Disease Presenting as Nonconvulsive Status Epilepticus. Case Reports in Neurological Medicine No. 2018 (2018), pp.1-4.
https://search.emarefa.net/detail/BIM-1145376
American Medical Association (AMA)
Rakitin, Aleksei& Vibo, R.& Veikat, Vaiko& Õunapuu, Anne& Liigant, Aive& Haldre, Sulev. Creutzfeldt-Jakob Disease Presenting as Nonconvulsive Status Epilepticus. Case Reports in Neurological Medicine. 2018. Vol. 2018, no. 2018, pp.1-4.
https://search.emarefa.net/detail/BIM-1145376
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1145376