A Rare Case of Angioimmunoblastic T-Cell Lymphoma with Epstein-Barr Virus-Negative Reed-Sternberg-Like B-Cells, Chylous Ascites, and Chylothorax

Joint Authors

Willemsen, Mathijs
Dielis, Arne W. J. H.
Samarska, Iryna V.
Koster, Ad
van Marion, Arienne M.

Source

Case Reports in Hematology

Issue

Vol. 2017, Issue 2017 (31 Dec. 2017), pp.1-6, 6 p.

Publisher

Hindawi Publishing Corporation

Publication Date

2017-04-12

Country of Publication

Egypt

No. of Pages

6

Main Subjects

Diseases

Abstract EN

Angioimmunoblastic T-cell lymphoma is a rare non-Hodgkin lymphoma with dismal prognosis.

The median age of presentation ranges from 62 to 69 years with generalized lymphadenopathy, B symptoms, and hepatosplenomegaly as the most prevalent symptoms.

The combination of B-cell and T-cell proliferations is common in AITL and the B-cell component may resemble Reed-Sternberg-like B-cells.

Epstein-Barr virus is estimated to be present in 80–95% of AITL biopsies.

Only a handful of EBV-negative AITL cases with EBV-negative RS-like B-cells have been reported over the last decade.

We present a rare case of EBV-negative AITL with chylous ascites and chylothorax.

Microscopic and immunohistochemical analysis revealed the presence of EBV-negative Reed-Sternberg-like B-cells in the tumor.

American Psychological Association (APA)

Willemsen, Mathijs& Dielis, Arne W. J. H.& Samarska, Iryna V.& Koster, Ad& van Marion, Arienne M.. 2017. A Rare Case of Angioimmunoblastic T-Cell Lymphoma with Epstein-Barr Virus-Negative Reed-Sternberg-Like B-Cells, Chylous Ascites, and Chylothorax. Case Reports in Hematology،Vol. 2017, no. 2017, pp.1-6.
https://search.emarefa.net/detail/BIM-1145750

Modern Language Association (MLA)

Willemsen, Mathijs…[et al.]. A Rare Case of Angioimmunoblastic T-Cell Lymphoma with Epstein-Barr Virus-Negative Reed-Sternberg-Like B-Cells, Chylous Ascites, and Chylothorax. Case Reports in Hematology No. 2017 (2017), pp.1-6.
https://search.emarefa.net/detail/BIM-1145750

American Medical Association (AMA)

Willemsen, Mathijs& Dielis, Arne W. J. H.& Samarska, Iryna V.& Koster, Ad& van Marion, Arienne M.. A Rare Case of Angioimmunoblastic T-Cell Lymphoma with Epstein-Barr Virus-Negative Reed-Sternberg-Like B-Cells, Chylous Ascites, and Chylothorax. Case Reports in Hematology. 2017. Vol. 2017, no. 2017, pp.1-6.
https://search.emarefa.net/detail/BIM-1145750

Data Type

Journal Articles

Language

English

Notes

Includes bibliographical references

Record ID

BIM-1145750