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Primary Epithelioid Sarcoma of Orbit: A Case Report and Review of the Literature
Joint Authors
Lee, Christopher M.
Wagner, Aaron
Kaya, Erin A.
Broadbent, Talmage J.
Thomas, Cheddhi J.
Thatcher, Steve H.
Fairbanks, Robert K.
Lamoreaux, Wayne T.
Source
Case Reports in Oncological Medicine
Issue
Vol. 2018, Issue 2018 (31 Dec. 2018), pp.1-6, 6 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2018-12-17
Country of Publication
Egypt
No. of Pages
6
Main Subjects
Abstract EN
Epithelioid sarcoma is a rare high-grade malignancy identified by Enzinger in 1970.
It accounts for 1% of all reported soft tissue sarcomas and presents most commonly in distal upper extremities in young adults with a male predominance.
At this time, there are only 5 previously reported cases of primary epithelioid sarcoma of the orbit.
We present a primary orbital epithelioid sarcoma case of a patient who underwent orbital exenteration followed by external beam radiation treatment.
Because the literature is limited, this is to our knowledge the largest descriptive analysis of cases of orbital epithelioid sarcoma.
We also provide a detailed review of all the previously reported primary orbital epithelioid sarcoma cases, as well as a discussion on the use of postoperative radiation therapy for patients with epithelioid sarcoma.
Surgical resection followed by adjuvant radiation therapy appears to be a safe option for local treatment of this rare malignancy, but further future studies are needed of this rare clinical situation in order to better understand and optimize treatment for patients with orbital epithelioid sarcoma.
American Psychological Association (APA)
Kaya, Erin A.& Broadbent, Talmage J.& Thomas, Cheddhi J.& Wagner, Aaron& Thatcher, Steve H.& Lamoreaux, Wayne T.…[et al.]. 2018. Primary Epithelioid Sarcoma of Orbit: A Case Report and Review of the Literature. Case Reports in Oncological Medicine،Vol. 2018, no. 2018, pp.1-6.
https://search.emarefa.net/detail/BIM-1146252
Modern Language Association (MLA)
Kaya, Erin A.…[et al.]. Primary Epithelioid Sarcoma of Orbit: A Case Report and Review of the Literature. Case Reports in Oncological Medicine No. 2018 (2018), pp.1-6.
https://search.emarefa.net/detail/BIM-1146252
American Medical Association (AMA)
Kaya, Erin A.& Broadbent, Talmage J.& Thomas, Cheddhi J.& Wagner, Aaron& Thatcher, Steve H.& Lamoreaux, Wayne T.…[et al.]. Primary Epithelioid Sarcoma of Orbit: A Case Report and Review of the Literature. Case Reports in Oncological Medicine. 2018. Vol. 2018, no. 2018, pp.1-6.
https://search.emarefa.net/detail/BIM-1146252
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1146252