Unilateral Enlarged Vestibular Aqueduct Syndrome and Bilateral Endolymphatic Hydrops
Joint Authors
Ralli, Massimo
Nola, Giuseppe
Sparvoli, Luca
Ralli, Giovanni
Source
Case Reports in Otolaryngology
Issue
Vol. 2017, Issue 2017 (31 Dec. 2017), pp.1-6, 6 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2017-05-18
Country of Publication
Egypt
No. of Pages
6
Main Subjects
Abstract EN
Enlarged vestibular aqueduct (EVA) syndrome is a common congenital inner ear malformation characterized by a vestibular aqueduct with a diameter larger than 1.5 mm, mixed or sensorineural hearing loss that ranges from mild to profound, and vestibular disorders that may be present with a range from mild imbalance to episodic objective vertigo.
In our study, we present the case of a patient with unilateral enlarged vestibular aqueduct and bilateral endolymphatic hydrops (EH).
EH was confirmed through anamnestic history and audiological exams; EVA was diagnosed using high-resolution CT scans and MRI images.
Therapy included intratympanic infusion of corticosteroids with a significant hearing improvement, more evident in the ear contralateral to EVA.
Although most probably unrelated, EVA and EH may present with similar symptoms and therefore the diagnostic workup should always include the proper steps to perform a correct diagnosis.
Association between progression of hearing loss and head trauma in patients with a diagnosis of EVA syndrome is still uncertain; however, these individuals should be advised to avoid activities that increase intracranial pressure to prevent further hearing deterioration.
Intratympanic treatment with steroids is a safe and well-tolerated procedure that has demonstrated its efficacy in hearing, tinnitus, and vertigo control in EH.
American Psychological Association (APA)
Ralli, Massimo& Nola, Giuseppe& Sparvoli, Luca& Ralli, Giovanni. 2017. Unilateral Enlarged Vestibular Aqueduct Syndrome and Bilateral Endolymphatic Hydrops. Case Reports in Otolaryngology،Vol. 2017, no. 2017, pp.1-6.
https://search.emarefa.net/detail/BIM-1148709
Modern Language Association (MLA)
Ralli, Massimo…[et al.]. Unilateral Enlarged Vestibular Aqueduct Syndrome and Bilateral Endolymphatic Hydrops. Case Reports in Otolaryngology No. 2017 (2017), pp.1-6.
https://search.emarefa.net/detail/BIM-1148709
American Medical Association (AMA)
Ralli, Massimo& Nola, Giuseppe& Sparvoli, Luca& Ralli, Giovanni. Unilateral Enlarged Vestibular Aqueduct Syndrome and Bilateral Endolymphatic Hydrops. Case Reports in Otolaryngology. 2017. Vol. 2017, no. 2017, pp.1-6.
https://search.emarefa.net/detail/BIM-1148709
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1148709