Severe Hepatopulmonary Syndrome in a Child with Caroli Syndrome
Joint Authors
Jon, Cindy
De Jesus-Rojas, W.
McBeth, K.
Yadav, A.
Stark, J. M.
Mosquera, Ricardo A.
Source
Issue
Vol. 2017, Issue 2017 (31 Dec. 2017), pp.1-4, 4 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2017-08-13
Country of Publication
Egypt
No. of Pages
4
Main Subjects
Abstract EN
Hepatopulmonary Syndrome (HPS) is a potential complication of chronic liver disease and is more commonly seen in the adult population.
Caroli Syndrome is a rare inherited disorder characterized by intrahepatic ductal dilation and liver fibrosis that leads to portal hypertension.
In children with liver disease, HPS should be considered in the differential diagnosis of prolonged, otherwise unexplained, hypoxemia.
The presence of HPS can improve patient priority on the liver transplantation wait list, despite their Pediatric End-Stage Liver Disease (PELD) score.
We present a 6-year-old girl with Caroli Syndrome and End-Stage Renal Disease who presented with persistent hypoxemia.
The goal of this report is to increase awareness of HPS in children.
American Psychological Association (APA)
De Jesus-Rojas, W.& McBeth, K.& Yadav, A.& Stark, J. M.& Mosquera, Ricardo A.& Jon, Cindy. 2017. Severe Hepatopulmonary Syndrome in a Child with Caroli Syndrome. Case Reports in Pediatrics،Vol. 2017, no. 2017, pp.1-4.
https://search.emarefa.net/detail/BIM-1149237
Modern Language Association (MLA)
De Jesus-Rojas, W.…[et al.]. Severe Hepatopulmonary Syndrome in a Child with Caroli Syndrome. Case Reports in Pediatrics No. 2017 (2017), pp.1-4.
https://search.emarefa.net/detail/BIM-1149237
American Medical Association (AMA)
De Jesus-Rojas, W.& McBeth, K.& Yadav, A.& Stark, J. M.& Mosquera, Ricardo A.& Jon, Cindy. Severe Hepatopulmonary Syndrome in a Child with Caroli Syndrome. Case Reports in Pediatrics. 2017. Vol. 2017, no. 2017, pp.1-4.
https://search.emarefa.net/detail/BIM-1149237
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1149237