Congenital Infantile Fibrosarcoma Causing Intestinal Perforation in a Newborn
Joint Authors
Till, Holger
Kaiser, Margarita
Sperl, Daniela
Nagy, Eszter
Singer, G.
Liegl-Atzwanger, Bernadette
Source
Issue
Vol. 2017, Issue 2017 (31 Dec. 2017), pp.1-3, 3 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2017-06-12
Country of Publication
Egypt
No. of Pages
3
Main Subjects
Abstract EN
Congenital infantile fibrosarcoma (CIF) is a rare malignant mesenchymal tumor and only 14 cases have been reported with gastrointestinal manifestation.
We report about a female newborn delivered per emergency cesarean section at 34 weeks of gestation.
Postnatally, she rapidly developed an acute abdomen and sonographic evidence of intestinal perforation requiring laparotomy on the first day of life.
A perforated 2 × 3 cm sized spherical tumorous structure of the jejunum was identified.
Due to unknown histopathology at this point and unclear resectional margins, she received a temporary ileostomy, which was closed two months later.
Histopathology revealed a congenital intestinal fibrosarcoma without the characteristic ETV6-NTRK3 fusion transcript.
In conclusion, this rare tumor must be considered as differential diagnosis of intestinal perforations in newborns.
American Psychological Association (APA)
Kaiser, Margarita& Liegl-Atzwanger, Bernadette& Nagy, Eszter& Sperl, Daniela& Singer, G.& Till, Holger. 2017. Congenital Infantile Fibrosarcoma Causing Intestinal Perforation in a Newborn. Case Reports in Pediatrics،Vol. 2017, no. 2017, pp.1-3.
https://search.emarefa.net/detail/BIM-1149282
Modern Language Association (MLA)
Kaiser, Margarita…[et al.]. Congenital Infantile Fibrosarcoma Causing Intestinal Perforation in a Newborn. Case Reports in Pediatrics No. 2017 (2017), pp.1-3.
https://search.emarefa.net/detail/BIM-1149282
American Medical Association (AMA)
Kaiser, Margarita& Liegl-Atzwanger, Bernadette& Nagy, Eszter& Sperl, Daniela& Singer, G.& Till, Holger. Congenital Infantile Fibrosarcoma Causing Intestinal Perforation in a Newborn. Case Reports in Pediatrics. 2017. Vol. 2017, no. 2017, pp.1-3.
https://search.emarefa.net/detail/BIM-1149282
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1149282