IgG4-Related Disease, the Malignancy Mimicker: Case Series from Bahrain
Joint Authors
Aljufairi, Eman Ali
Haider, Majeed
Haji, Fatima
Alalwan, Osama
Shah, Tejal S.
Source
Issue
Vol. 2018, Issue 2018 (31 Dec. 2018), pp.1-9, 9 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2018-10-28
Country of Publication
Egypt
No. of Pages
9
Main Subjects
Abstract EN
IgG4-related disease is an evolving immune-mediated condition.
The hallmark of this condition is IgG4(+) plasma cells infiltration of the affected organs accompanied by a variable degree of fibrosis and occasionally elevated serum IgG4 level.
It links many conditions that were once recognized as isolated unrelated idiopathic single organ disorders (e.g., autoimmune pancreatitis, Mikulicz syndrome, and retroperitoneal fibrosis) under one umbrella.
It usually presents clinically as tumor-like swelling of the involved organs that can be misdiagnosed as neoplasia.
In this case series, we present four cases that were considered as neoplasia but turned out to be IgG4-related disease, we demonstrate the protean manifestations of this condition and variable organs involvement, and we share our experience in using rituximab as the steroid sparing immunosuppressant agent to control this disease.
American Psychological Association (APA)
Haider, Majeed& Haji, Fatima& Alalwan, Osama& Aljufairi, Eman Ali& Shah, Tejal S.. 2018. IgG4-Related Disease, the Malignancy Mimicker: Case Series from Bahrain. Case Reports in Rheumatology،Vol. 2018, no. 2018, pp.1-9.
https://search.emarefa.net/detail/BIM-1149811
Modern Language Association (MLA)
Haider, Majeed…[et al.]. IgG4-Related Disease, the Malignancy Mimicker: Case Series from Bahrain. Case Reports in Rheumatology No. 2018 (2018), pp.1-9.
https://search.emarefa.net/detail/BIM-1149811
American Medical Association (AMA)
Haider, Majeed& Haji, Fatima& Alalwan, Osama& Aljufairi, Eman Ali& Shah, Tejal S.. IgG4-Related Disease, the Malignancy Mimicker: Case Series from Bahrain. Case Reports in Rheumatology. 2018. Vol. 2018, no. 2018, pp.1-9.
https://search.emarefa.net/detail/BIM-1149811
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1149811