![](/images/graphics-bg.png)
Erdheim-Chester Disease and Small Lymphocytic Lymphoma Collision Tumour Presenting as a Perirenal Mass
Joint Authors
Maietta, Antonio
Razmpoosh, Maryam
Source
Issue
Vol. 2020, Issue 2020 (31 Dec. 2020), pp.1-6, 6 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2020-04-15
Country of Publication
Egypt
No. of Pages
6
Main Subjects
Abstract EN
Background.
Erdheim-Chester disease is a rare histiocytic neoplasm associated with MAPK pathway mutations.
Disease manifestation is variable often involving many different organs, mainly bone, retroperitoneum, the heart, and the central nervous system.
Histological findings include foamy histiocytes in a fibrous stroma with scattered inflammatory infiltrate.
Histiocytes are CD68 positive and S100 negative.
Case Report.
We report a case of Erdheim-Chester disease associated with small lymphocytic lymphoma presenting as a perirenal mass with a review of the recent literature.
Conclusions.
Erdheim-Chester disease rarely can be associated with other cancers, namely myeloid neoplasms.
We report a case of Erdheim-Chester disease presenting with small lymphocytic lymphoma as a perirenal mass.
The association of Erdheim-Chester disease with lymphoproliferative disorders needs to be elucidated.
American Psychological Association (APA)
Maietta, Antonio& Razmpoosh, Maryam. 2020. Erdheim-Chester Disease and Small Lymphocytic Lymphoma Collision Tumour Presenting as a Perirenal Mass. Case Reports in Pathology،Vol. 2020, no. 2020, pp.1-6.
https://search.emarefa.net/detail/BIM-1150402
Modern Language Association (MLA)
Maietta, Antonio& Razmpoosh, Maryam. Erdheim-Chester Disease and Small Lymphocytic Lymphoma Collision Tumour Presenting as a Perirenal Mass. Case Reports in Pathology No. 2020 (2020), pp.1-6.
https://search.emarefa.net/detail/BIM-1150402
American Medical Association (AMA)
Maietta, Antonio& Razmpoosh, Maryam. Erdheim-Chester Disease and Small Lymphocytic Lymphoma Collision Tumour Presenting as a Perirenal Mass. Case Reports in Pathology. 2020. Vol. 2020, no. 2020, pp.1-6.
https://search.emarefa.net/detail/BIM-1150402
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1150402