Giant Perineal Solitary Fibrous Tumor: A Rare Case Report

Abstract EN

Background.

Solitary fibrous tumor (SFT) is a fibroblastic mesenchymal tumor that was initially described from the pleura but currently arises at almost every anatomic site.

It is usually benign, and surgical resection is curative.

SFT involving the perineum is extremely rare.

This is the third case report of a perineal SFT in the literature.

Case Presentation.

We reported an uncommon case of a 64-year-old man presenting with a huge perineal mass that started growing 3 years before his arrival in our service.

He was asymptomatic.

A contrast-enhanced CT scan revealed a heterogeneous well-circumscribed perineal mass with soft-tissue density.

Invasion of the surrounding organs, distal metastasis, and lymph node swelling were absent.

The complete resection of mass was done successfully.

The specimen was a 23.0 × 14.0 × 8.0 cm encapsulated tumor.

Mass weight was 1,170 g.

After pathological analysis, we confirmed that the mass was a solitary fibrous tumor.

The diagnosis was based on clinical findings and histological morphology and immunohistochemistry study.

Conclusion.

SFTs are usually indolent tumors with a favorable prognosis.

The perineal location is extremely rare.

Complete resection of the mass is the treatment of choice.