Successful Liposteroid Therapy for a Recurrent Idiopathic Pulmonary Hemosiderosis with Down Syndrome
Joint Authors
Tobai, Hiromi
Yano, Jun
Sato, Norio
Amanuma, Fumitaka
Takahashi, Mikio
Endo, Mikiya
Ishimura, Masataka
Ohga, Shouichi
Maruyama, Hidekazu
Source
Issue
Vol. 2020, Issue 2020 (31 Dec. 2020), pp.1-5, 5 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2020-04-25
Country of Publication
Egypt
No. of Pages
5
Main Subjects
Abstract EN
Idiopathic pulmonary hemosiderosis (IPH) is a rare and life-threatening disorder.
Early diagnosis and appropriate management are essential for their better prognosis and patients’ quality of life (QOL).
It is considered that Down syndrome patients with IPH have a worse prognosis compared to other IPH cases.
A 2-year-old girl with Down syndrome received the diagnosis of IPH after two episodes of massive pulmonary hemorrhage requiring assist ventilation, who suffered from recurrent IPH during tapering period of oral corticosteroid, started liposteroid therapy.
We report here a case of successful control of recurrent IPH and improved QOL enormously with tapering dose of corticosteroid after starting liposteroid therapy.
American Psychological Association (APA)
Tobai, Hiromi& Yano, Jun& Sato, Norio& Amanuma, Fumitaka& Takahashi, Mikio& Endo, Mikiya…[et al.]. 2020. Successful Liposteroid Therapy for a Recurrent Idiopathic Pulmonary Hemosiderosis with Down Syndrome. Case Reports in Pediatrics،Vol. 2020, no. 2020, pp.1-5.
https://search.emarefa.net/detail/BIM-1150645
Modern Language Association (MLA)
Tobai, Hiromi…[et al.]. Successful Liposteroid Therapy for a Recurrent Idiopathic Pulmonary Hemosiderosis with Down Syndrome. Case Reports in Pediatrics No. 2020 (2020), pp.1-5.
https://search.emarefa.net/detail/BIM-1150645
American Medical Association (AMA)
Tobai, Hiromi& Yano, Jun& Sato, Norio& Amanuma, Fumitaka& Takahashi, Mikio& Endo, Mikiya…[et al.]. Successful Liposteroid Therapy for a Recurrent Idiopathic Pulmonary Hemosiderosis with Down Syndrome. Case Reports in Pediatrics. 2020. Vol. 2020, no. 2020, pp.1-5.
https://search.emarefa.net/detail/BIM-1150645
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1150645