Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis
Joint Authors
Alzughayyar, Tareq Z.
Abukhalaf, Sadi A.
Dandis, Beesan W.
Za’tari, Tasnim
Amro, Adham M.
Rajabi, Yazan A.
Source
Issue
Vol. 2020, Issue 2020 (31 Dec. 2020), pp.1-5, 5 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2020-05-20
Country of Publication
Egypt
No. of Pages
5
Main Subjects
Abstract EN
Background.
FMF is a common disease in the Mediterranean populations and may be complicated by AA amyloidosis.
The coexistence of adrenal and thyroid amyloidosis in AA amyloidosis secondary to familial Mediterranean fever (FMF) is an extremely rare reported condition.
We presented a previously unreported triad of adrenal, thyroid, and cardiac amyloidosis secondary to FMF.
Presentation of Case.
We reported a 23-year-old Palestinian male patient presented with hypotension, vomiting, diarrhea, and abdominal pain.
The patient was subsequently diagnosed to have an adrenal crisis with both amyloid goiter and cardiac amyloidosis.
Conclusion.
It is crucial to recognize the adrenal crisis in patients with AA amyloidosis secondary to FMF who present similarly to acute FMF inflammatory episodes.
The adrenal crisis has high morbidity and mortality, especially if not recognized early in the course of the disease.
American Psychological Association (APA)
Abukhalaf, Sadi A.& Dandis, Beesan W.& Za’tari, Tasnim& Amro, Adham M.& Alzughayyar, Tareq Z.& Rajabi, Yazan A.. 2020. Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis. Case Reports in Rheumatology،Vol. 2020, no. 2020, pp.1-5.
https://search.emarefa.net/detail/BIM-1151174
Modern Language Association (MLA)
Abukhalaf, Sadi A.…[et al.]. Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis. Case Reports in Rheumatology No. 2020 (2020), pp.1-5.
https://search.emarefa.net/detail/BIM-1151174
American Medical Association (AMA)
Abukhalaf, Sadi A.& Dandis, Beesan W.& Za’tari, Tasnim& Amro, Adham M.& Alzughayyar, Tareq Z.& Rajabi, Yazan A.. Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis. Case Reports in Rheumatology. 2020. Vol. 2020, no. 2020, pp.1-5.
https://search.emarefa.net/detail/BIM-1151174
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1151174