Kidney Transplantation for Erdheim-Chester Disease
Joint Authors
Yoo, Jongwon
Gunsteen, Cynthia
Patel, Sima
Clevy-Schneller, Ted
Nand, Sucha
Jain, Divya
Garcia-Roca, Raquel
Desai, Amishi
Akkina, Sanjeev
Source
Case Reports in Transplantation
Issue
Vol. 2020, Issue 2020 (31 Dec. 2020), pp.1-4, 4 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2020-07-13
Country of Publication
Egypt
No. of Pages
4
Main Subjects
Abstract EN
Erdheim-Chester disease is a rare inflammatory disease that infiltrates skeletal and extra-skeletal tissue.
Chronic kidney disease (CKD) in Erdheim-Chester disease is usually attributed to retroperitoneal lesions that lead to urologic obstruction and hydronephrosis.
In this report, we describe a patient diagnosed with Erdheim-Chester disease who eventually developed end-stage kidney disease (ESKD).
After complete remission of Erdheim-Chester disease by vemurafenib therapy and 2 years of hemodialysis, the patient underwent a deceased donor kidney transplantation with basiliximab induction and tacrolimus/mycophenolic acid maintenance.
After conversion of mycophenolic acid to azathioprine due to cost, acute cellular rejection had occurred, and he was treated with steroid therapy.
The patient remained in complete remission from Erdheim-Chester disease and dialysis-free 16 months after transplant.
Kidney transplantation is another treatment option for those patients with Erdheim-Chester disease who suffer from renal failure in the setting of complete remission.
American Psychological Association (APA)
Yoo, Jongwon& Gunsteen, Cynthia& Patel, Sima& Clevy-Schneller, Ted& Nand, Sucha& Jain, Divya…[et al.]. 2020. Kidney Transplantation for Erdheim-Chester Disease. Case Reports in Transplantation،Vol. 2020, no. 2020, pp.1-4.
https://search.emarefa.net/detail/BIM-1151684
Modern Language Association (MLA)
Yoo, Jongwon…[et al.]. Kidney Transplantation for Erdheim-Chester Disease. Case Reports in Transplantation No. 2020 (2020), pp.1-4.
https://search.emarefa.net/detail/BIM-1151684
American Medical Association (AMA)
Yoo, Jongwon& Gunsteen, Cynthia& Patel, Sima& Clevy-Schneller, Ted& Nand, Sucha& Jain, Divya…[et al.]. Kidney Transplantation for Erdheim-Chester Disease. Case Reports in Transplantation. 2020. Vol. 2020, no. 2020, pp.1-4.
https://search.emarefa.net/detail/BIM-1151684
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1151684