Modified le fort i osteotomy and genioplasty for management of severe dentofacial deformity in β-thalassaemia major : case report and review of the literature
Other Title(s)
تعديل في القطع العظمي لوفور 1 و رأب الذقن لعلاج تشوه سني وجهي حاد لحالة مصابة بأنيميا البحر المتوسط الكبرى : تقرير حالة مراجعة أدبية
Joint Authors
Bakathir, Abd al-Aziz A.
al-Hashimi, Ahmad Karim
al-Rawahi, Badir
al-Husni, Khamis M.
al-Bakri, Abd Allah
Source
Sultan Qaboos University Medical Journal
Issue
Vol. 20, Issue 3 (31 Aug. 2020), pp.362-367, 6 p.
Publisher
Sultan Qaboos University College of Medicine and Health Sciences
Publication Date
2020-08-31
Country of Publication
Oman
No. of Pages
6
Main Subjects
Abstract EN
β-thalassaemia major is an autosomal recessive form of haemoglobinopathy that is characterised by complete lack of production of the β-chains resulting in multiple complications that include severe anaemia, failure to thrive and skeletal abnormalities.
facial deformities induced by β-thalassaemia major are rare and are very challenging to treat from a surgical point of view.
we report a 33-year-old female patient with β-thalassaemia major who presented to the dental & maxillofacial surgery department, sultan Qaboos university hospital, Muscat, Oman, in 2017 with gross dentofacial skeletal deformity contributing to her psychosocial issues.
the facial deformity was corrected surgically by excision of the enlarged maxilla, modified le fort i osteotomy and advancement genioplasty.
this case highlights the pre-operative preparation, surgical management, encountered complications and treatment outcome within 24 months of follow-up.
American Psychological Association (APA)
al-Husni, Khamis M.& Bakathir, Abd al-Aziz A.& al-Hashimi, Ahmad Karim& al-Rawahi, Badir& al-Bakri, Abd Allah. 2020. Modified le fort i osteotomy and genioplasty for management of severe dentofacial deformity in β-thalassaemia major : case report and review of the literature. Sultan Qaboos University Medical Journal،Vol. 20, no. 3, pp.362-367.
https://search.emarefa.net/detail/BIM-1366065
Modern Language Association (MLA)
al-Husni, Khamis M.…[et al.]. Modified le fort i osteotomy and genioplasty for management of severe dentofacial deformity in β-thalassaemia major : case report and review of the literature. Sultan Qaboos University Medical Journal Vol. 20, no. 3 (Aug. 2020), pp.362-367.
https://search.emarefa.net/detail/BIM-1366065
American Medical Association (AMA)
al-Husni, Khamis M.& Bakathir, Abd al-Aziz A.& al-Hashimi, Ahmad Karim& al-Rawahi, Badir& al-Bakri, Abd Allah. Modified le fort i osteotomy and genioplasty for management of severe dentofacial deformity in β-thalassaemia major : case report and review of the literature. Sultan Qaboos University Medical Journal. 2020. Vol. 20, no. 3, pp.362-367.
https://search.emarefa.net/detail/BIM-1366065
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references : p. 367
Record ID
BIM-1366065