Renal AA amyloidosis in a patient with hereditary complete complement C4 deficiency
Joint Authors
Ghushah, Rim
al-Yunus, Fathi
Ben Maiz, Hedi
Khidr, Adil
Bin Hamidah, Fathi
Source
Saudi Journal of Kidney Diseases and Transplantation
Issue
Vol. 22, Issue 5 (31 Oct. 2011), pp.1008-1011, 4 p.
Publisher
Saudi Center for Organ Transplantation
Publication Date
2011-10-31
Country of Publication
Saudi Arabia
No. of Pages
4
Main Subjects
Topics
Abstract EN
Hereditary complete C4 deficiency has until now been reported in 30 cases only.
A disturbed clearance of immune- complexes probably predisposes these individuals to systemic lupus erythematous, other immune- complex diseases and recurrent microbial infections.
We present here a 20- year- old female with hereditary complete C4 deficiency.
Renal biopsy demonstrated renal AA amyloidosis.
This unique case further substantiates that deficiency of classical pathway components predisposes to the development of recurrent microbial infections and that the patients may develop AA amyloidosis.
Furthermore, in clinical practice, the nephritis syndrome occurring in a patient with hereditary complete complement C4 deficiency should lead to the suspicion of renal AA amyloidosis.
American Psychological Association (APA)
Ghushah, Rim& Bin Hamidah, Fathi& al-Yunus, Fathi& Ben Maiz, Hedi& Khidr, Adil. 2011. Renal AA amyloidosis in a patient with hereditary complete complement C4 deficiency. Saudi Journal of Kidney Diseases and Transplantation،Vol. 22, no. 5, pp.1008-1011.
https://search.emarefa.net/detail/BIM-268162
Modern Language Association (MLA)
Ghushah, Rim…[et al.]. Renal AA amyloidosis in a patient with hereditary complete complement C4 deficiency. Saudi Journal of Kidney Diseases and Transplantation Vol. 22, no. 5 (Oct. 2011), pp.1008-1011.
https://search.emarefa.net/detail/BIM-268162
American Medical Association (AMA)
Ghushah, Rim& Bin Hamidah, Fathi& al-Yunus, Fathi& Ben Maiz, Hedi& Khidr, Adil. Renal AA amyloidosis in a patient with hereditary complete complement C4 deficiency. Saudi Journal of Kidney Diseases and Transplantation. 2011. Vol. 22, no. 5, pp.1008-1011.
https://search.emarefa.net/detail/BIM-268162
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references : p. 1010-1011
Record ID
BIM-268162