Giant renal artery pseudoaneurysm caused by rupture of renal angiomyolipoma following pregnancy : endovascular treatment andreview of the literature

Abstract EN

Renal angiomyolipoma is a hamartomatous, benign tumor composed of blood vessels, fatty tissue and smooth muscle cells, and is often detected incidentally.

It can also be associated with the tuberous-sclerosis complex (TSC).

Pregnancy and use of oral contraceptives are known to be associated with an increased risk of tumoral rupture and bleeding.

Herein, we report a unique case of renal angiomyolipoma associated with TSC who presented with hypovolemic shock as a result of spontaneous rupture of a giant renal pseudoaneurysm, immediately after pregnancy.

Emergency endovascular treatment was successful with sparing of most of the affected kidney as demonstrated by follow-up computed tomography imaging.