Scleroma : new patterns and approaches to an old disease

Abstract EN

Background: Scleroma is a chronic granulomatous condition that particularly affects the nose in all patients and the larynx in fewer patients, and less often the trachea and bronchi.

Study design: Analysing the clinical and imaging data of 48 patients’ scleroma.

Results: Forty-eight scleroma patients were included.

Their age ranged from 17 to 60 years.

There was female predominance.

Patients presented with laryngeal and tracheal symptomatologies were more common than nasal symptomatology.

Combined nasal with laryngeal affection exhibited the most frequent occurrence.

Radiologically, a new pattern of involvement of the trachea fits the description of cribriform tracheitis.

The commonest naked eye appearance was fibrosis, granuloma and to a lesser extent atrophy and crusting.

Conclusion: A change in the pattern of presentation and regional involvement in scleroma dictated the need for a change of its name and our awareness.