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Susac's Syndrome in a Patient Diagnosed with MS for 20 Years : A Case Report
Joint Authors
Irkec, Ceyla
Zeynep Batur Caglayan, Hale
Akyol, Asli
Yildirim-Capraz, Irem
Nazliel, Bijen
Source
Case Reports in Neurological Medicine
Issue
Vol. 2014, Issue 2014 (31 Dec. 2014), pp.1-4, 4 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2014-02-02
Country of Publication
Egypt
No. of Pages
4
Main Subjects
Abstract EN
Susac’s syndrome is an uncommon neurologic disorder of unknown cause.
It has been described as a clinical triad of encephalopathy, hearing loss, and branch retinal artery occlusions.
Clinically the diagnosis is difficult when the patient presents only a portion of a triad.
We present a case with vision loss and sensorineural deafness and who had been diagnosed with MS for 20 years.
Susac’s syndrome is presumed to be an autoimmune endotheliopathy.
Neurologic symptoms and signs are diffuse and multifocal, acute or subacute in onset, and progress during the active phase of the disease.
In some patients the onset was stroke like and in others that of subacute dementia.
Headache, often with migrainous features, was a prominent feature initially in more than one half of the patients.
A high index of suspicion leading to correct diagnosis and early appropriate therapy may reduce the permanent sequel seen with this disease.
Misdiagnosis is common.
In patients in whom diagnosis and treatment are delayed permanent morbidity is higher in terms of visual loss, hearing loss, and neurologic debility.
In patients in whom rapid diagnosis has led to early administration of immunosuppressive therapy, recovery can be almost complete.
American Psychological Association (APA)
Nazliel, Bijen& Akyol, Asli& Zeynep Batur Caglayan, Hale& Yildirim-Capraz, Irem& Irkec, Ceyla. 2014. Susac's Syndrome in a Patient Diagnosed with MS for 20 Years : A Case Report. Case Reports in Neurological Medicine،Vol. 2014, no. 2014, pp.1-4.
https://search.emarefa.net/detail/BIM-455131
Modern Language Association (MLA)
Nazliel, Bijen…[et al.]. Susac's Syndrome in a Patient Diagnosed with MS for 20 Years : A Case Report. Case Reports in Neurological Medicine No. 2014 (2014), pp.1-4.
https://search.emarefa.net/detail/BIM-455131
American Medical Association (AMA)
Nazliel, Bijen& Akyol, Asli& Zeynep Batur Caglayan, Hale& Yildirim-Capraz, Irem& Irkec, Ceyla. Susac's Syndrome in a Patient Diagnosed with MS for 20 Years : A Case Report. Case Reports in Neurological Medicine. 2014. Vol. 2014, no. 2014, pp.1-4.
https://search.emarefa.net/detail/BIM-455131
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-455131