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Vulvar Malignancy in Neurofibromatosis Syndrome
Joint Authors
Musella, Angela
Domenici, Lavinia
Casorelli, Assunta
Palaia, Innocenza
Panici, Pierluigi Benedetti
Martoccia, Angela
Source
Case Reports in Obstetrics and Gynecology
Issue
Vol. 2013, Issue 2013 (31 Dec. 2013), pp.1-3, 3 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2013-09-19
Country of Publication
Egypt
No. of Pages
3
Main Subjects
Abstract EN
Type 1 neurofibromatosis (NF1) is a dominantly inherited neurologic disorder that affects primarily the skin, bones, and peripheral nervous system.
It may be associated with a variety of clinical manifestations including cafe-au-lait spots, skinfold freckling, Lisch nodules, and visceral neurofibromas.
Individuals affected by NF1 harbor an increased risk for both benign and malignant tumors.
Malignant transformation is usually observed in the form of neurosarcoma.
Rarely, NF1 affects the genital tract, and isolated vulvar localization is extremely rare.
Here is reported a rare case of a solitary neurosarcoma of the vulva in a 43-year-old woman affected by NF1 syndrome treated with surgical excision.
The purpose of this case is to underline the possibility of association between NF1 and genital tract sarcoma and to suggest an accurate evaluation of rapid growth vulvar mass in this setting.
American Psychological Association (APA)
Musella, Angela& Palaia, Innocenza& Domenici, Lavinia& Casorelli, Assunta& Martoccia, Angela& Panici, Pierluigi Benedetti. 2013. Vulvar Malignancy in Neurofibromatosis Syndrome. Case Reports in Obstetrics and Gynecology،Vol. 2013, no. 2013, pp.1-3.
https://search.emarefa.net/detail/BIM-455447
Modern Language Association (MLA)
Musella, Angela…[et al.]. Vulvar Malignancy in Neurofibromatosis Syndrome. Case Reports in Obstetrics and Gynecology No. 2013 (2013), pp.1-3.
https://search.emarefa.net/detail/BIM-455447
American Medical Association (AMA)
Musella, Angela& Palaia, Innocenza& Domenici, Lavinia& Casorelli, Assunta& Martoccia, Angela& Panici, Pierluigi Benedetti. Vulvar Malignancy in Neurofibromatosis Syndrome. Case Reports in Obstetrics and Gynecology. 2013. Vol. 2013, no. 2013, pp.1-3.
https://search.emarefa.net/detail/BIM-455447
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-455447