Exercise Stress Testing in Children with Metabolic or Neuromuscular Disorders

Joint Authors

Visser, Gepke
Helders, Paul J.
van Hasselt, Peter M.
Prinsen, Berthil H.
Ernsting, Cornelia G.
Groen, Wim G.
Hulzebos, Erik H.
Takken, Tim

Source

International Journal of Pediatrics

Issue

Vol. 2010, Issue 2010 (31 Dec. 2010), pp.1-6, 6 p.

Publisher

Hindawi Publishing Corporation

Publication Date

2010-07-15

Country of Publication

Egypt

No. of Pages

6

Main Subjects

Medicine

Abstract EN

The role of exercise as a diagnostic or therapeutic tool in patients with a metabolic disease (MD) or neuromuscular disorder (NMD) is relatively underresearched.

In this paper we describe the metabolic profiles during exercise in 13 children (9 boys, 4 girls, age 5–15 yrs) with a diagnosed MD or NMD.

Graded cardiopulmonary exercise tests and/or a 90-min prolonged submaximal exercise test were performed.

During exercise, respiratory gas-exchange and heart rate were monitored; blood and urine samples were collected for biochemical analysis at set time points.

Several characteristics in our patient group were observed, which reflected the differences in pathophysiology of the various disorders.

Metabolic profiles during exercises CPET and PXT seem helpful in the evaluation of patients with a MD or NMD.

American Psychological Association (APA)

Takken, Tim& Groen, Wim G.& Hulzebos, Erik H.& Ernsting, Cornelia G.& van Hasselt, Peter M.& Prinsen, Berthil H.…[et al.]. 2010. Exercise Stress Testing in Children with Metabolic or Neuromuscular Disorders. International Journal of Pediatrics،Vol. 2010, no. 2010, pp.1-6.
https://search.emarefa.net/detail/BIM-457801

Modern Language Association (MLA)

Takken, Tim…[et al.]. Exercise Stress Testing in Children with Metabolic or Neuromuscular Disorders. International Journal of Pediatrics No. 2010 (2010), pp.1-6.
https://search.emarefa.net/detail/BIM-457801

American Medical Association (AMA)

Takken, Tim& Groen, Wim G.& Hulzebos, Erik H.& Ernsting, Cornelia G.& van Hasselt, Peter M.& Prinsen, Berthil H.…[et al.]. Exercise Stress Testing in Children with Metabolic or Neuromuscular Disorders. International Journal of Pediatrics. 2010. Vol. 2010, no. 2010, pp.1-6.
https://search.emarefa.net/detail/BIM-457801

Data Type

Journal Articles

Language

English

Notes

Includes bibliographical references

Record ID

BIM-457801