Left Ventricle Diverticulum with Partial Cantrell's Syndrome

Abstract EN

Cantrell syndrome is a very rare congenital disease associating five features: a midline, upper abdominal wall disorder, lower sternal abnormality, anterior diaphragmatic defect, diaphragmatic pericardial abnormality, and congenital abnormalities of the heart.

In this paper, we report a case of partial Cantrell's syndrome with left ventricular diverticulum, triatrial situs solitus, ventricular septal defect, dextrorotation of the heart, an anterior pericardial diaphragmatic defect, and a midline supraumbilical abdominal wall defect with umbilical hernia.

The 5-month-old patient underwent a successful cardiac surgical procedure.

A PTFE membrane was placed on the apex of the heart to facilitate reopening of the patient’s chest.

Postoperative course was uneventful.

The patient was discharged with good clinical condition and with a normal cardiac function.