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Hypoxemic Bronchiolitis Related to Major Histocompatibility Class II Deficiency
Joint Authors
Besbès, H.
Lajmi, Khaled
Meriem, Ch. B.
Ghédira, L.
Hammami, Saber
Hadded, S.
Guédiche, Mohamed Néji
Source
Issue
Vol. 2013, Issue 2013 (31 Dec. 2013), pp.1-3, 3 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2013-08-24
Country of Publication
Egypt
No. of Pages
3
Main Subjects
Abstract EN
Major histocompatibility complex class II expression deficiency is an autosomal recessive primary combined immunodeficiency.
The prevalence of this deficiency is the highest in Mediterranean areas, especially North Africa.
Early diagnosis is essential due to high mortality in the first 2 years of life.
Prognosis is very poor when bone marrow transplantation cannot be performed.
We report the case of an infant with major histocompatibility complex class II expression deficiency revealed by hypoxemic bronchiolitis due to Pneumocystis jiroveci.
American Psychological Association (APA)
Hammami, Saber& Besbès, H.& Hadded, S.& Lajmi, Khaled& Ghédira, L.& Meriem, Ch. B.…[et al.]. 2013. Hypoxemic Bronchiolitis Related to Major Histocompatibility Class II Deficiency. Case Reports in Medicine،Vol. 2013, no. 2013, pp.1-3.
https://search.emarefa.net/detail/BIM-462785
Modern Language Association (MLA)
Hammami, Saber…[et al.]. Hypoxemic Bronchiolitis Related to Major Histocompatibility Class II Deficiency. Case Reports in Medicine No. 2013 (2013), pp.1-3.
https://search.emarefa.net/detail/BIM-462785
American Medical Association (AMA)
Hammami, Saber& Besbès, H.& Hadded, S.& Lajmi, Khaled& Ghédira, L.& Meriem, Ch. B.…[et al.]. Hypoxemic Bronchiolitis Related to Major Histocompatibility Class II Deficiency. Case Reports in Medicine. 2013. Vol. 2013, no. 2013, pp.1-3.
https://search.emarefa.net/detail/BIM-462785
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-462785