Giant Malignant Pheochromocytoma with Palpable Rib Metastases

Abstract EN

Pheochromocytoma is a rare and usually benign neuroendocrine neoplasm.

Only 10% of all these tumors are malignant and there are no definitive histological or cytological criteria of malignancy.

Single malignancy criteria are the presence of advanced locoregional disease or metastases.

We report a case, with a giant retroperitoneal tumor having multiple metastases including palpable rib metastases, who was diagnosed as a malignant pheochromocytoma.

The patient was treated with surgery.

The literature was reviewed to evaluate tumor features and current diagnostic and therapeutic approaches for patients with metastatic or potentially malignant pheochromocytoma.