A Rare Case of Endolymphatic Sac Tumour : Clinicopathologic Study and Surgical Management
Joint Authors
Ferri, Emanuele
Armato, Enrico
Amadori, Maurizio
Pavon, Ida
Source
Case Reports in Otolaryngology
Issue
Vol. 2014, Issue 2014 (31 Dec. 2014), pp.1-6, 6 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2014-06-04
Country of Publication
Egypt
No. of Pages
6
Main Subjects
Abstract EN
Objective.
Endolymphatic sac tumor (ELST) is a rare neoplasm arising from the intrapetrous portion of the endolymphatic sac, either isolated or in association with the von Hippel-Lindau disease.
We report a sporadic case of ELST with an overview of the literature and a discussion of clinic-radiological, histopathologic, and surgical findings.
Case Report.
A young woman presented with a progressive hearing loss in the left ear.
Otoscopy showed a reddish, bleeding hypotympanic mass.
CT demonstrated an expansile lytic mastoid lesion extending to the middle ear, with bone erosion.
MRI confirmed a lesion of increased signal on T1-weighted sequences.
The patient underwent a canal wall-down tympanoplasty with complete removal of the tumor.
Histopathology was consistent with a papillary ELST.
Immunohistochemistry was positive for cytokeratin and chromogranin A.
Conclusion.
This paper highlights the rarity of ELST, the need for an accurate neuroradiological and immunohistochemical study at the early stages, and the timeliness of surgical treatment.
American Psychological Association (APA)
Ferri, Emanuele& Amadori, Maurizio& Armato, Enrico& Pavon, Ida. 2014. A Rare Case of Endolymphatic Sac Tumour : Clinicopathologic Study and Surgical Management. Case Reports in Otolaryngology،Vol. 2014, no. 2014, pp.1-6.
https://search.emarefa.net/detail/BIM-467256
Modern Language Association (MLA)
Ferri, Emanuele…[et al.]. A Rare Case of Endolymphatic Sac Tumour : Clinicopathologic Study and Surgical Management. Case Reports in Otolaryngology No. 2014 (2014), pp.1-6.
https://search.emarefa.net/detail/BIM-467256
American Medical Association (AMA)
Ferri, Emanuele& Amadori, Maurizio& Armato, Enrico& Pavon, Ida. A Rare Case of Endolymphatic Sac Tumour : Clinicopathologic Study and Surgical Management. Case Reports in Otolaryngology. 2014. Vol. 2014, no. 2014, pp.1-6.
https://search.emarefa.net/detail/BIM-467256
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-467256