The Rendu-Osler-Weber Disease Revealed by a Refractory Hypoxemia and Severe Cerebral Fat Embolism
Joint Authors
Amiel, Jean-Bernard
Barreto, Leonel
Dugard, Anthony
Vignon, Philippe
Pichon, Nicolas
François, Bruno
Clavel, Marc
Source
Issue
Vol. 2013, Issue 2013 (31 Dec. 2013), pp.1-3, 3 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2013-08-01
Country of Publication
Egypt
No. of Pages
3
Main Subjects
Abstract EN
The Rendu-Osler-Weber disease is a genetic disease which may lead to severe hemorrhage and less frequently to severe organ dysfunction.
We report the case of a 22-year-old patient with no personal medical history who was involved in a motorcycle accident and exhibited severe complications related to large arteriovenous pulmonary shunts during his ICU stay.
The patient developed an unexplained severe hypoxemia which was attributed to several arteriovenous shunts of the pulmonary vasculature by a contrast study during a transesophageal echocardiographic examination.
The course was subsequently complicated by a prolonged coma associated with hemiplegia which was attributed to a massive paradoxical fat embolism in the setting of an untreated femoral fracture.
In addition to hemorrhagic complications which may lead to intractable shock, arteriovenous malformations associated with the Rendu-Osler-Weber disease may involve the pulmonary vasculature and result in unexpected complications, such as hypoxemia or severe cerebral fat embolism in high-risk patients.
American Psychological Association (APA)
Barreto, Leonel& Amiel, Jean-Bernard& Dugard, Anthony& Pichon, Nicolas& Clavel, Marc& François, Bruno…[et al.]. 2013. The Rendu-Osler-Weber Disease Revealed by a Refractory Hypoxemia and Severe Cerebral Fat Embolism. Case Reports in Critical Care،Vol. 2013, no. 2013, pp.1-3.
https://search.emarefa.net/detail/BIM-471975
Modern Language Association (MLA)
Barreto, Leonel…[et al.]. The Rendu-Osler-Weber Disease Revealed by a Refractory Hypoxemia and Severe Cerebral Fat Embolism. Case Reports in Critical Care No. 2013 (2013), pp.1-3.
https://search.emarefa.net/detail/BIM-471975
American Medical Association (AMA)
Barreto, Leonel& Amiel, Jean-Bernard& Dugard, Anthony& Pichon, Nicolas& Clavel, Marc& François, Bruno…[et al.]. The Rendu-Osler-Weber Disease Revealed by a Refractory Hypoxemia and Severe Cerebral Fat Embolism. Case Reports in Critical Care. 2013. Vol. 2013, no. 2013, pp.1-3.
https://search.emarefa.net/detail/BIM-471975
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-471975