Hereditary Hemorrhagic Telangiectasia Presenting as High Output Cardiac Failure during Pregnancy

Abstract EN

High-output cardiac failure secondary to hepatic involvement is a rare complication of hereditary hemorrhagic telangiectasia (HHT).

Here we report a 43-year-old woman who presented at 29 weeks gestation of her second pregnancy with complications of right-sided heart failure and preterm labor.

After delivery via cesarean section, the patient was found to have intrahepatic arteriovenous malformations through non-invasive imaging.

Subsequently, a family history of vascular malformations and epistaxis was elucidated and a diagnosis of HHT was made.

This case is presented, along with a review of the literature and discussion of hepatic involvement in HHT with particular focus on the pregnant patient.