Perivascular Epithelioid Cell Tumor of the Ileum Presenting as Diverticulitis
Joint Authors
Unluoglu, Saime
Bayol, Umit
Ozenen, Bekir
Pala, Emel Ebru
Korkmaz, Nilay
Ipekci, Fuat
Source
Issue
Vol. 2012, Issue 2012 (31 Dec. 2012), pp.1-4, 4 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2012-04-29
Country of Publication
Egypt
No. of Pages
4
Main Subjects
Abstract EN
Perivascular epithelioid cell tumors (PEComas) are a group of rare mesenchymal neoplasms.
Gastrointestinal PEComas are exceptionally rare, there being only a few case reports in the literature involving the colon and small intestine.
Nearly all PEComas show immunoreactivity for both melanocytic (HMB45 and/or Melan-A) and smooth muscle (actin and/or desmin) markers.
A 36-year-old male was admitted to the hospital with acut- abdomen.
At laparatomy, a nodular mass protruding from the ileum which clinically simulated a diverticulitis was noticed.
Gross examination of the specimen revealed a 2×1,5×1 cm secondarily ulcerated, solid, nodular, gray white tumor mass in the ileal wall.
Histologically, tumor cells were composed of nests of round-polygonal epithelioid cells with abundant clear to slightly eosinophilic granular cytoplasm and round vesicular nuclei.
The nests were separated by thin fibrovascular septa.
Minimal necrosis and low mitotic activity were noticed in the tumor.
Immunohistochemically, tumor cells were positive for SMA, HMB45, and Melan-A and negative for CD10, RCC, CD45, CD117, CD34, EMA, and Desmin.
Diagnosis was PEComa of the ileum.
We report the case of ileal PEComa to remind the unusual presentation (diverticulitis) of these tumors, besides rarity and diagnostic difficulties.
American Psychological Association (APA)
Unluoglu, Saime& Bayol, Umit& Korkmaz, Nilay& Ozenen, Bekir& Ipekci, Fuat& Pala, Emel Ebru. 2012. Perivascular Epithelioid Cell Tumor of the Ileum Presenting as Diverticulitis. Case Reports in Pathology،Vol. 2012, no. 2012, pp.1-4.
https://search.emarefa.net/detail/BIM-474677
Modern Language Association (MLA)
Unluoglu, Saime…[et al.]. Perivascular Epithelioid Cell Tumor of the Ileum Presenting as Diverticulitis. Case Reports in Pathology No. 2012 (2012), pp.1-4.
https://search.emarefa.net/detail/BIM-474677
American Medical Association (AMA)
Unluoglu, Saime& Bayol, Umit& Korkmaz, Nilay& Ozenen, Bekir& Ipekci, Fuat& Pala, Emel Ebru. Perivascular Epithelioid Cell Tumor of the Ileum Presenting as Diverticulitis. Case Reports in Pathology. 2012. Vol. 2012, no. 2012, pp.1-4.
https://search.emarefa.net/detail/BIM-474677
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-474677