Congenital Portal Vein Aneurysm Associated with Peliosis Hepatis and Intestinal Lymphangiectasia
Joint Authors
Mungan, Zeynel
Baran, Bulent
Pinarbasi, Binnur
Gulluoglu, Mine
Bakir, Baris
Demir, Kadir
Kaymakoglu, Sabahattin
Akyuz, Filiz
Source
Gastroenterology Research and Practice
Issue
Vol. 2009, Issue 2009 (31 Dec. 2009), pp.1-5, 5 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2010-03-30
Country of Publication
Egypt
No. of Pages
5
Main Subjects
Abstract EN
Portal vein aneurisym (PVA), peliosis hepatis (PH) and intestinal lymphangiectasia (IL) all are very uncommon entities.
Herein, we presented a unique patient with these three rare entities who was admitted to our hospital because of portal hypertensive ascites rich in protein and lymphocyte.
PVA was extrahepatic and associated with coronary vein aneurysm.
Peliosis hepatis was of microscopic form.
Lymphangiectasia was present in peritoneum and small intestine.
Diagnoses of these rare entities were made by imaging techniques and histopathological findings.
Patient also had hydronephrosis caused by ureteropelvic junction narrowing.
Best of our knowledge, there is no such a case reported previously with the association of PVA, PH and IL.
Therefore, we propose PVAPHIL syndrome to define this novel association.
American Psychological Association (APA)
Mungan, Zeynel& Pinarbasi, Binnur& Bakir, Baris& Gulluoglu, Mine& Baran, Bulent& Akyuz, Filiz…[et al.]. 2010. Congenital Portal Vein Aneurysm Associated with Peliosis Hepatis and Intestinal Lymphangiectasia. Gastroenterology Research and Practice،Vol. 2009, no. 2009, pp.1-5.
https://search.emarefa.net/detail/BIM-474796
Modern Language Association (MLA)
Mungan, Zeynel…[et al.]. Congenital Portal Vein Aneurysm Associated with Peliosis Hepatis and Intestinal Lymphangiectasia. Gastroenterology Research and Practice No. 2009 (2009), pp.1-5.
https://search.emarefa.net/detail/BIM-474796
American Medical Association (AMA)
Mungan, Zeynel& Pinarbasi, Binnur& Bakir, Baris& Gulluoglu, Mine& Baran, Bulent& Akyuz, Filiz…[et al.]. Congenital Portal Vein Aneurysm Associated with Peliosis Hepatis and Intestinal Lymphangiectasia. Gastroenterology Research and Practice. 2010. Vol. 2009, no. 2009, pp.1-5.
https://search.emarefa.net/detail/BIM-474796
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-474796