Angiosarcoma of Small Bowel Presenting with Obstruction : Novel Observations on a Rare Diagnostic Entity with Unique Clinical Presentation

Abstract EN

We present a case of angiosarcoma in small bowel, presenting with partial small bowel obstruction in a 79-year-old man with no history of radiation, chemotherapy, toxin exposure, or previous operative intervention.

Angiosarcoma of small bowel is a rare entity which may present with nausea, abdominal pain, recurrent bleeding, and usually a history of prior radiation or exposure to specific toxins (polyvinyl chloride).

Angiosarcoma of small bowel tends to spread rapidly and has a poor prognosis.

We review the surgical and oncologic challenges.

We report unique macroscopic findings of raised hyperemic margins, which are suggestive of a vasogenic lesion and the histologic feature of a partially retiform pattern with dense basement membrane material in an otherwise poorly differentiated lesion.