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Cardiac Epithelioid PEComa : Report of Two Cases and Review of the Literature
Joint Authors
Niu, Huilin
Bing, Zhanyong
Zhang, Paul J.
Wang, F. W.
Source
Issue
Vol. 2012, Issue 2012 (31 Dec. 2012), pp.1-6, 6 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2012-09-03
Country of Publication
Egypt
No. of Pages
6
Main Subjects
Abstract EN
Cardiac PEComa is very rare.
We reported two cases of epithelioid PEComas, one in an adult and one in a 2-year-old child.
Both tumors were composed of sheets of epithelioid cells with coagulation necrosis.
In addition, the adult case showed marked nuclear atypia and high mitotic activity with atypical mitosis and the pediatric case showed unusual clear cell features.
Immunohistochemically, both tumors were positive for HMB-45 and SMA and negative for S100 and cytokeratin.
Electron microscopy was performed in the pediatric case and showed premelanosomes.
The adult patient developed extensive metastasis indicating malignant behavior.
Prior to the two cases, only 5 other cases of cardiac PEComa were reported and the literatures are reviewed.
American Psychological Association (APA)
Niu, Huilin& Wang, F. W.& Zhang, Paul J.& Bing, Zhanyong. 2012. Cardiac Epithelioid PEComa : Report of Two Cases and Review of the Literature. Case Reports in Medicine،Vol. 2012, no. 2012, pp.1-6.
https://search.emarefa.net/detail/BIM-478367
Modern Language Association (MLA)
Niu, Huilin…[et al.]. Cardiac Epithelioid PEComa : Report of Two Cases and Review of the Literature. Case Reports in Medicine No. 2012 (2012), pp.1-6.
https://search.emarefa.net/detail/BIM-478367
American Medical Association (AMA)
Niu, Huilin& Wang, F. W.& Zhang, Paul J.& Bing, Zhanyong. Cardiac Epithelioid PEComa : Report of Two Cases and Review of the Literature. Case Reports in Medicine. 2012. Vol. 2012, no. 2012, pp.1-6.
https://search.emarefa.net/detail/BIM-478367
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-478367