A Case of Neurosarcoidosis with Labyrinthine Involvement
Joint Authors
Saindane, Amit Manohar
Smith, Myrton
Johnson, Peter B.
Melbourne-Chambers, Roxanne
Desai, Nilesh
Source
Issue
Vol. 2014, Issue 2014 (31 Dec. 2014), pp.1-5, 5 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2014-03-06
Country of Publication
Egypt
No. of Pages
5
Main Subjects
Abstract EN
Sarcoidosis is a chronic granulomatous disease of unknown aetiology, which may involve any organ system.
It most commonly occurs in adults with childhood involvement being rare.
Central nervous system involvement is seen in up to 25% and typically involves meningeal disease resulting in multiple cranial neuropathies.
Other common clinical findings include seizures, headache, dementia, and pituitary dysfunction.
Imaging plays a central role in the diagnosis with typical findings including pachymeningeal and leptomeningeal enhancing lesions.
Other imaging findings include lacunar and major territory infarcts, hypothalamic and infundibular thickening, hydrocephalus, and cranial nerve enhancement.
We present a case of an eight-year-old male patient with progressive headache, visual disturbance, unilateral sensory hearing loss, and multiple cranial neuropathies.
Imaging findings demonstrated the classic pachymeningeal and leptomeningeal enhancement along much of the skull base, as well as enhancement of the right and left second and eighth cranial nerves.
Extensive inflammatory changes were noted in the temporal bones and paranasal sinuses.
There was also enhancement of the right and left labyrinths.
Sinus biopsy confirmed sarcoidosis.
We present the first case to our knowledge of sarcoid labyrinthitis.
American Psychological Association (APA)
Johnson, Peter B.& Melbourne-Chambers, Roxanne& Saindane, Amit Manohar& Desai, Nilesh& Smith, Myrton. 2014. A Case of Neurosarcoidosis with Labyrinthine Involvement. Case Reports in Radiology،Vol. 2014, no. 2014, pp.1-5.
https://search.emarefa.net/detail/BIM-479083
Modern Language Association (MLA)
Johnson, Peter B.…[et al.]. A Case of Neurosarcoidosis with Labyrinthine Involvement. Case Reports in Radiology No. 2014 (2014), pp.1-5.
https://search.emarefa.net/detail/BIM-479083
American Medical Association (AMA)
Johnson, Peter B.& Melbourne-Chambers, Roxanne& Saindane, Amit Manohar& Desai, Nilesh& Smith, Myrton. A Case of Neurosarcoidosis with Labyrinthine Involvement. Case Reports in Radiology. 2014. Vol. 2014, no. 2014, pp.1-5.
https://search.emarefa.net/detail/BIM-479083
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-479083