Malignant Mesenteric Perivascular Epithelioid Cell Neoplasm Presenting as an Intra-Abdominal Fistula in a 49-Year-Old Female
Joint Authors
Levin, Miles B.
Kapur, Sakshi
Patel, Napoleon K.
Huang, Richard
Source
Case Reports in Oncological Medicine
Issue
Vol. 2014, Issue 2014 (31 Dec. 2014), pp.1-5, 5 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2014-07-09
Country of Publication
Egypt
No. of Pages
5
Main Subjects
Abstract EN
Perivascular epithelioid cell tumors are rare mesenchymal tumors arising from histologically and immunohistochemically distinctive perivascular epithelioid cells that express both myogenic and melanocytic markers.
These tumors are known to arise from different organs in the body and usually have an unpredictable clinical course.
We report a case of a 49-year-old female who presented with diffuse abdominal pain, fever, chills, and nonbilious vomiting for a day.
Work-up revealed a mesenteric mass measuring 13.5×7.7×9.5 cm, arising in the mesentery of the hepatic flexure, with adjacent gas suggestive of fistularization into the right colon.
An exploratory laparotomy with resection of the mesenteric mass was performed, and the initial histopathology results were compatible with either an adenocarcinoma or a sarcoma; however, because of poor differentiation it was difficult to make a definitive diagnosis.
However, final histopathology results revealed a malignant perivascular epithelioid cell tumor (with reservation that a S100 negative metastatic melanoma must be excluded clinically).
Following surgery the patient was started on everolimus, an m-TOR inhibitor, and has shown good response to this medication.
American Psychological Association (APA)
Kapur, Sakshi& Patel, Napoleon K.& Levin, Miles B.& Huang, Richard. 2014. Malignant Mesenteric Perivascular Epithelioid Cell Neoplasm Presenting as an Intra-Abdominal Fistula in a 49-Year-Old Female. Case Reports in Oncological Medicine،Vol. 2014, no. 2014, pp.1-5.
https://search.emarefa.net/detail/BIM-479335
Modern Language Association (MLA)
Kapur, Sakshi…[et al.]. Malignant Mesenteric Perivascular Epithelioid Cell Neoplasm Presenting as an Intra-Abdominal Fistula in a 49-Year-Old Female. Case Reports in Oncological Medicine No. 2014 (2014), pp.1-5.
https://search.emarefa.net/detail/BIM-479335
American Medical Association (AMA)
Kapur, Sakshi& Patel, Napoleon K.& Levin, Miles B.& Huang, Richard. Malignant Mesenteric Perivascular Epithelioid Cell Neoplasm Presenting as an Intra-Abdominal Fistula in a 49-Year-Old Female. Case Reports in Oncological Medicine. 2014. Vol. 2014, no. 2014, pp.1-5.
https://search.emarefa.net/detail/BIM-479335
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-479335