Isolated Ventricular Noncompaction Syndrome in a Nigerian Male : Case Report and Review of the Literature

Abstract EN

Isolated ventricular non-compaction cardiomyopathy (IVNC) is a rare, morphologically distinct primary genetic cardiomyopathy, which is now gaining prominence as an important differential diagnosis in patients presenting with cardiac failure.

We describe a case report of a Nigerian male with facial dysmorphism presenting with cardiac failure.

This is followed by a review of the literature with focus on the diagnosis of this condition, which may be difficult especially in non-Caucasian populations.