Combined Liver and Kidney Transplant in a Patient with Budd-Chiari Syndrome Secondary to Autosomal Dominant Polycystic Kidney Disease Associated with Polycystic Liver Disease : Report of a Case with a 9-Year Follow-Up

Abstract EN

Polycystic liver disease (PLD) is a hereditary disease inherited by autosomal dominant trait that occurs as a frequent extrarenal manifestation of autosomal dominant polycystic kidney disease (ADPKD).

We report a case of a 59-year-old woman diagnosed with ADPKD associated with PLD.

End-stage chronic renal failure with a secondary Budd-Chiari syndrome developed during the patient’s clinical course.

She underwent combined liver and kidney transplantation, with a successful response over a 9-year follow-up period.