Pulmonary Alveolar Proteinosis in Association with Congenital Dyserythropoietic Anemia : A Case Report
Joint Authors
Carden, Marcus A.
Barman, Ashish
Massey, G. V.
Source
Issue
Vol. 2012, Issue 2012 (31 Dec. 2012), pp.1-3, 3 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2012-06-28
Country of Publication
Egypt
No. of Pages
3
Main Subjects
Abstract EN
A two-year-old girl with congenital dyserythropoietic anemia (CDA) acutely developed fever, tachypnea, and increased oxygen requirement.
Chest X-ray revealed bilateral interstitial infiltrates and mild cardiomegaly.
Blood cultures grew no infectious agents, while pulmonary specimens grew cytomegalovirus (CMV).
Treatment with intravenous ganciclovir was initiated but without response.
Final cytologic preparations of bronchoalveolar lavage (BAL) fluid revealed eosinophilic amorphous material consistent with pulmonary alveolar proteinosis (PAP).
CDA and PAP are extremely rare disorders in pediatrics.
PAP should be considered in patients with hematological disorders who present with acute interstitial pneumonia, after infectious causes are ruled out.
American Psychological Association (APA)
Carden, Marcus A.& Barman, Ashish& Massey, G. V.. 2012. Pulmonary Alveolar Proteinosis in Association with Congenital Dyserythropoietic Anemia : A Case Report. Case Reports in Pediatrics،Vol. 2012, no. 2012, pp.1-3.
https://search.emarefa.net/detail/BIM-486066
Modern Language Association (MLA)
Carden, Marcus A.…[et al.]. Pulmonary Alveolar Proteinosis in Association with Congenital Dyserythropoietic Anemia : A Case Report. Case Reports in Pediatrics No. 2012 (2012), pp.1-3.
https://search.emarefa.net/detail/BIM-486066
American Medical Association (AMA)
Carden, Marcus A.& Barman, Ashish& Massey, G. V.. Pulmonary Alveolar Proteinosis in Association with Congenital Dyserythropoietic Anemia : A Case Report. Case Reports in Pediatrics. 2012. Vol. 2012, no. 2012, pp.1-3.
https://search.emarefa.net/detail/BIM-486066
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-486066