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Malignant Rhabdoid Tumour of the Liver in the Young Adult : Report of First Two Cases
Joint Authors
Nobili, Cinzia
Lermite, Emilie
Pessaux, Patrick
Teyssedou, Carlos
Bachellier, Philippe
Arnaud, Jean-Pierre
Marzano, Ettore
Source
Issue
Vol. 2009, Issue 2009 (31 Dec. 2009), pp.1-4, 4 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2009-09-10
Country of Publication
Egypt
No. of Pages
4
Main Subjects
Abstract EN
Few cases of malignant rhabdoid tumour (MRT) of the liver are reported in literature and always in paediatric patients.
We report the first two cases of young adults submitted to hepatic resection for MRT of the liver.
A major liver resection was performed in both cases.
The histology showed round or fusiform, loosely cohesive cells.
The cytoplasm contained abundant eosinophilic inclusions, which caused the nuclei to be located in eccentric locations, giving the characteristic rhabdoid appearance.
The immunohistochemical study was performed, and characteristic lack of nuclear INI1 protein expression was found.
In a case surgery was associated to chemoradiotherapy.
One patient died at 48 months followup for tumour recurrence.
The other is still alive at 25 months followup.
MRTs are rare tumours of pediatric age with poor prognosis.
Hypothetical less malignant behaviour in the young adults could be supposed.
Therefore an aggressive surgical and oncological treatment seems justified.
American Psychological Association (APA)
Marzano, Ettore& Lermite, Emilie& Nobili, Cinzia& Teyssedou, Carlos& Bachellier, Philippe& Arnaud, Jean-Pierre…[et al.]. 2009. Malignant Rhabdoid Tumour of the Liver in the Young Adult : Report of First Two Cases. HPB Surgery،Vol. 2009, no. 2009, pp.1-4.
https://search.emarefa.net/detail/BIM-486361
Modern Language Association (MLA)
Marzano, Ettore…[et al.]. Malignant Rhabdoid Tumour of the Liver in the Young Adult : Report of First Two Cases. HPB Surgery No. 2009 (2009), pp.1-4.
https://search.emarefa.net/detail/BIM-486361
American Medical Association (AMA)
Marzano, Ettore& Lermite, Emilie& Nobili, Cinzia& Teyssedou, Carlos& Bachellier, Philippe& Arnaud, Jean-Pierre…[et al.]. Malignant Rhabdoid Tumour of the Liver in the Young Adult : Report of First Two Cases. HPB Surgery. 2009. Vol. 2009, no. 2009, pp.1-4.
https://search.emarefa.net/detail/BIM-486361
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-486361