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Staged, Open, No-Ischemia Nephron-Sparing Surgery for Bilateral-Multiple Kidney Tumors in a Patient with Birt-Hogg-Dubé Syndrome
Joint Authors
Akkaya, Ayşe Deniz
Vural, Metin
Musaoglu, Ahmet
Cezayirli, Fatin
Peker, Kamil
Gümüş, Terman
Esen, Tarık
Tefekli, Ahmet H.
Source
Issue
Vol. 2012, Issue 2012 (31 Dec. 2012), pp.1-6, 6 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2012-04-24
Country of Publication
Egypt
No. of Pages
6
Main Subjects
Abstract EN
Hereditary kidney cancer patients with bilateral multiple kidney tumors represent challenges in the era of rapidly growing minimal invasive treatment techniques.
Birt-Hogg-Dubé Syndrome (BHDS) is an autosomal dominant genodermatosis characterized by a triad of benign skin tumors (fibrofolliculomas, trichodiscomas, acrochordons) together with an increased risk of developing malignant renal tumors and pulmonary disease such as pneumothoraces and multiple lung cysts.
The morbidity and mortality of the affected patients is determined by the presence of the kidney tumors, which tend to be multifocal and bilateral, as observed in other hereditary kidney cancer syndromes like von Hippel-Lindau disease, familial leiomyomatosis, and hereditary papillary renal cell carcinoma.
Herein, a patient with BHDS, presenting with synchronous bilateral multiple kidney tumors, is reported.
The report describes the management of kidney tumors with two-stage open nephron-sparing surgery in which the nonvascular clamping technique was utilized.
American Psychological Association (APA)
Tefekli, Ahmet H.& Akkaya, Ayşe Deniz& Peker, Kamil& Gümüş, Terman& Vural, Metin& Cezayirli, Fatin…[et al.]. 2012. Staged, Open, No-Ischemia Nephron-Sparing Surgery for Bilateral-Multiple Kidney Tumors in a Patient with Birt-Hogg-Dubé Syndrome. Case Reports in Medicine،Vol. 2012, no. 2012, pp.1-6.
https://search.emarefa.net/detail/BIM-487353
Modern Language Association (MLA)
Tefekli, Ahmet H.…[et al.]. Staged, Open, No-Ischemia Nephron-Sparing Surgery for Bilateral-Multiple Kidney Tumors in a Patient with Birt-Hogg-Dubé Syndrome. Case Reports in Medicine No. 2012 (2012), pp.1-6.
https://search.emarefa.net/detail/BIM-487353
American Medical Association (AMA)
Tefekli, Ahmet H.& Akkaya, Ayşe Deniz& Peker, Kamil& Gümüş, Terman& Vural, Metin& Cezayirli, Fatin…[et al.]. Staged, Open, No-Ischemia Nephron-Sparing Surgery for Bilateral-Multiple Kidney Tumors in a Patient with Birt-Hogg-Dubé Syndrome. Case Reports in Medicine. 2012. Vol. 2012, no. 2012, pp.1-6.
https://search.emarefa.net/detail/BIM-487353
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-487353