Inflammatory Myofibroblastic Tumor of the Right Atrium

Joint Authors

Eising, Gregory P.
Trudel, Michel
Lange, Peter
Khan, Javed A.
Von Canal, Friederike
Saleh, Moataz A.
Augustin, Norbert
Jha, Neerod K.
al-Sousi, Awatif
al-Mahmid, Wail
Misra, Virendra K.

Source

Case Reports in Medicine

Issue

Vol. 2010, Issue 2010 (31 Dec. 2010), pp.1-4, 4 p.

Publisher

Hindawi Publishing Corporation

Publication Date

2010-09-19

Country of Publication

Egypt

No. of Pages

4

Main Subjects

Medicine

Abstract EN

Cardiac inflammatory myofibroblastic tumor (IMT) is a rare entity and is associated with distinct clinical, pathological and molecular features.

The clinical behavior, natural history, biological potential, management and prognosis of such tumors are unclear.

We present herewith an adolescent girl who presented with similar entity involving the junction of the right atrium and the inferior vena cava (IVC) in association with thrombocytosis and IVC thrombosis leading to obstruction of blood flow.

Diagnostic tools included imaging and immuno-histopathology studies.

Surgical management included resection of the tumor and thrombo-embolectomy of the IVC under cardiopulmonary bypass.

This case is unique due to association of complete obstruction of IVC caused by the strategic location of the tumor, thrombosis of vena cava and association of thrombocytosis.

These features have not been reported yet in relation to the cardiac IMT.

This report will help in better understanding and management of similar cases in terms of planning cannulation of femoral veins or application of total hypothermic circulatory arrest during cardiopulmonary bypass and prompt us to look for recurrence or metastasis during follow up using echocardiography and laboratory investigations.

The possibility of IMT should be kept in the differential diagnosis of cardiac tumors especially in children and adolescents.

American Psychological Association (APA)

Jha, Neerod K.& Trudel, Michel& Eising, Gregory P.& Lange, Peter& al-Sousi, Awatif& al-Mahmid, Wail…[et al.]. 2010. Inflammatory Myofibroblastic Tumor of the Right Atrium. Case Reports in Medicine،Vol. 2010, no. 2010, pp.1-4.
https://search.emarefa.net/detail/BIM-491254

Modern Language Association (MLA)

Jha, Neerod K.…[et al.]. Inflammatory Myofibroblastic Tumor of the Right Atrium. Case Reports in Medicine No. 2010 (2010), pp.1-4.
https://search.emarefa.net/detail/BIM-491254

American Medical Association (AMA)

Jha, Neerod K.& Trudel, Michel& Eising, Gregory P.& Lange, Peter& al-Sousi, Awatif& al-Mahmid, Wail…[et al.]. Inflammatory Myofibroblastic Tumor of the Right Atrium. Case Reports in Medicine. 2010. Vol. 2010, no. 2010, pp.1-4.
https://search.emarefa.net/detail/BIM-491254

Data Type

Journal Articles

Language

English

Notes

Includes bibliographical references

Record ID

BIM-491254