Inflammatory Myofibroblastic Tumor of the Right Atrium
Joint Authors
Eising, Gregory P.
Trudel, Michel
Lange, Peter
Khan, Javed A.
Von Canal, Friederike
Saleh, Moataz A.
Augustin, Norbert
Jha, Neerod K.
al-Sousi, Awatif
al-Mahmid, Wail
Misra, Virendra K.
Source
Issue
Vol. 2010, Issue 2010 (31 Dec. 2010), pp.1-4, 4 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2010-09-19
Country of Publication
Egypt
No. of Pages
4
Main Subjects
Abstract EN
Cardiac inflammatory myofibroblastic tumor (IMT) is a rare entity and is associated with distinct clinical, pathological and molecular features.
The clinical behavior, natural history, biological potential, management and prognosis of such tumors are unclear.
We present herewith an adolescent girl who presented with similar entity involving the junction of the right atrium and the inferior vena cava (IVC) in association with thrombocytosis and IVC thrombosis leading to obstruction of blood flow.
Diagnostic tools included imaging and immuno-histopathology studies.
Surgical management included resection of the tumor and thrombo-embolectomy of the IVC under cardiopulmonary bypass.
This case is unique due to association of complete obstruction of IVC caused by the strategic location of the tumor, thrombosis of vena cava and association of thrombocytosis.
These features have not been reported yet in relation to the cardiac IMT.
This report will help in better understanding and management of similar cases in terms of planning cannulation of femoral veins or application of total hypothermic circulatory arrest during cardiopulmonary bypass and prompt us to look for recurrence or metastasis during follow up using echocardiography and laboratory investigations.
The possibility of IMT should be kept in the differential diagnosis of cardiac tumors especially in children and adolescents.
American Psychological Association (APA)
Jha, Neerod K.& Trudel, Michel& Eising, Gregory P.& Lange, Peter& al-Sousi, Awatif& al-Mahmid, Wail…[et al.]. 2010. Inflammatory Myofibroblastic Tumor of the Right Atrium. Case Reports in Medicine،Vol. 2010, no. 2010, pp.1-4.
https://search.emarefa.net/detail/BIM-491254
Modern Language Association (MLA)
Jha, Neerod K.…[et al.]. Inflammatory Myofibroblastic Tumor of the Right Atrium. Case Reports in Medicine No. 2010 (2010), pp.1-4.
https://search.emarefa.net/detail/BIM-491254
American Medical Association (AMA)
Jha, Neerod K.& Trudel, Michel& Eising, Gregory P.& Lange, Peter& al-Sousi, Awatif& al-Mahmid, Wail…[et al.]. Inflammatory Myofibroblastic Tumor of the Right Atrium. Case Reports in Medicine. 2010. Vol. 2010, no. 2010, pp.1-4.
https://search.emarefa.net/detail/BIM-491254
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-491254