Neurologic Involvement in Scleroderma en Coup de Sabre
Joint Authors
Peres, Fernando Augusto
Amaral, Tiago Nardi
Guirau, Caio Rodrigues
Marques Neto, João Francisco
Lapa, Aline Tamires
Appenzeller, Simone
Source
Issue
Vol. 2012, Issue 2012 (31 Dec. 2012), pp.1-6, 6 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2012-01-27
Country of Publication
Egypt
No. of Pages
6
Main Subjects
Abstract EN
Localized scleroderma is a rare disease, characterized by sclerotic lesions.
A variety of presentations have been described, with different clinical characteristics and specific prognosis.
In scleroderma en coup de sabre (LScs) the atrophic lesion in frontoparietal area is the disease hallmark.
Skin and subcutaneous are the mainly affected tissues, but case reports of muscle, cartilage, and bone involvement are frequent.
These cases pose a difficult differential diagnosis with Parry-Romberg syndrome.
Once considered an exclusive cutaneous disorder, the neurologic involvement present in LScs has been described in several case reports.
Seizures are most frequently observed, but focal neurologic deficits, movement disorders, trigeminal neuralgia, and mimics of hemiplegic migraines have been reported.
Computed tomography and magnetic resonance imaging have aided the characterization of central nervous system lesions, and cerebral angiograms have pointed to vasculitis as a part of disease pathogenesis.
In this paper we describe the clinical and radiologic aspects of neurologic involvement in LScs.
American Psychological Association (APA)
Amaral, Tiago Nardi& Marques Neto, João Francisco& Lapa, Aline Tamires& Peres, Fernando Augusto& Guirau, Caio Rodrigues& Appenzeller, Simone. 2012. Neurologic Involvement in Scleroderma en Coup de Sabre. Autoimmune Diseases،Vol. 2012, no. 2012, pp.1-6.
https://search.emarefa.net/detail/BIM-493195
Modern Language Association (MLA)
Amaral, Tiago Nardi…[et al.]. Neurologic Involvement in Scleroderma en Coup de Sabre. Autoimmune Diseases No. 2012 (2012), pp.1-6.
https://search.emarefa.net/detail/BIM-493195
American Medical Association (AMA)
Amaral, Tiago Nardi& Marques Neto, João Francisco& Lapa, Aline Tamires& Peres, Fernando Augusto& Guirau, Caio Rodrigues& Appenzeller, Simone. Neurologic Involvement in Scleroderma en Coup de Sabre. Autoimmune Diseases. 2012. Vol. 2012, no. 2012, pp.1-6.
https://search.emarefa.net/detail/BIM-493195
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-493195