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Acute Pancreatitis with Rapid Clinical Improvement in a Child with Isovaleric Acidemia
Joint Authors
Tsouvala, Emmanouela
Evangeliou, Athanassios
Chatzimichael, Athanassios
Mantadakis, Elpis
Chrysafis, Ioannis
Source
Issue
Vol. 2013, Issue 2013 (31 Dec. 2013), pp.1-3, 3 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2013-02-04
Country of Publication
Egypt
No. of Pages
3
Main Subjects
Abstract EN
Isovaleric acidemia is a rare branched-chain organic acidemia.
The authors describe a 3.5-year-old girl with isovaleric acidemia and acute abdominal pain associated with bilious emesis.
Elevated serum amylase and abdominal ultrasonography demonstrating an enlarged and edematous pancreas, along with the presence of peripancreatic exudates, confirmed the presence of acute pancreatitis.
The patient recovered quickly with intravenous hydration, pancreatic rest, and administration of intravenous L-carnitine.
Pancreatitis should be ruled out in the context of vomiting in any patient with isovaleric acidemia.
Conversely, branched-chain organic acidemias should be included in the differential diagnosis of any child with pancreatitis of unknown origin.
American Psychological Association (APA)
Mantadakis, Elpis& Chrysafis, Ioannis& Tsouvala, Emmanouela& Evangeliou, Athanassios& Chatzimichael, Athanassios. 2013. Acute Pancreatitis with Rapid Clinical Improvement in a Child with Isovaleric Acidemia. Case Reports in Pediatrics،Vol. 2013, no. 2013, pp.1-3.
https://search.emarefa.net/detail/BIM-493385
Modern Language Association (MLA)
Mantadakis, Elpis…[et al.]. Acute Pancreatitis with Rapid Clinical Improvement in a Child with Isovaleric Acidemia. Case Reports in Pediatrics No. 2013 (2013), pp.1-3.
https://search.emarefa.net/detail/BIM-493385
American Medical Association (AMA)
Mantadakis, Elpis& Chrysafis, Ioannis& Tsouvala, Emmanouela& Evangeliou, Athanassios& Chatzimichael, Athanassios. Acute Pancreatitis with Rapid Clinical Improvement in a Child with Isovaleric Acidemia. Case Reports in Pediatrics. 2013. Vol. 2013, no. 2013, pp.1-3.
https://search.emarefa.net/detail/BIM-493385
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-493385