Perilobar Nephroblastomatosis : Natural History and Management

Joint Authors

Printza, N.
Papachristou, F.
Koliouskas, D.
Gombakis, N.
Matis, A.
Dotis, J.
Stabouli, S.

Source

Case Reports in Pediatrics

Issue

Vol. 2014, Issue 2014 (31 Dec. 2014), pp.1-7, 7 p.

Publisher

Hindawi Publishing Corporation

Publication Date

2014-07-09

Country of Publication

Egypt

No. of Pages

7

Main Subjects

Medicine

Abstract EN

Nephroblastomatosis (NB) has been considered as a precursor of Wilms tumor (WT).

The natural history of NB seems to present significant variation as some lesions may regress spontaneously, while others may grow and expand or relapse and develop into WT later in childhood.

Although, most investigators suggest adjutant chemotherapy, the effect and duration of treatment are not well established.

Children with diffuse perilobar NB, Beckwith-Wiedemann syndrome, and hemihypertrophy seem to particularly benefit from treatment.

We discuss our experience on two cases of NB and we review the literature for the management of this rare condition.

American Psychological Association (APA)

Stabouli, S.& Printza, N.& Dotis, J.& Matis, A.& Koliouskas, D.& Gombakis, N.…[et al.]. 2014. Perilobar Nephroblastomatosis : Natural History and Management. Case Reports in Pediatrics،Vol. 2014, no. 2014, pp.1-7.
https://search.emarefa.net/detail/BIM-496280

Modern Language Association (MLA)

Stabouli, S.…[et al.]. Perilobar Nephroblastomatosis : Natural History and Management. Case Reports in Pediatrics No. 2014 (2014), pp.1-7.
https://search.emarefa.net/detail/BIM-496280

American Medical Association (AMA)

Stabouli, S.& Printza, N.& Dotis, J.& Matis, A.& Koliouskas, D.& Gombakis, N.…[et al.]. Perilobar Nephroblastomatosis : Natural History and Management. Case Reports in Pediatrics. 2014. Vol. 2014, no. 2014, pp.1-7.
https://search.emarefa.net/detail/BIM-496280

Data Type

Journal Articles

Language

English

Notes

Includes bibliographical references

Record ID

BIM-496280