Successful Kidney Transplantation for End-Stage Renal Disease in Marfan's Syndrome
Joint Authors
Nozaki, Taiji
Hirano, Hajime
Yoshida, Kazuhiko
Sawada, Yugo
Shimizu, Tomokazu
Omoto, Kazuya
Ryosaka, Makoto
Tanabe, Kazunari
Ishida, Hideki
Source
Case Reports in Transplantation
Issue
Vol. 2013, Issue 2013 (31 Dec. 2013), pp.1-4, 4 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2013-09-04
Country of Publication
Egypt
No. of Pages
4
Main Subjects
Abstract EN
Marfan’s syndrome is a systemic disorder of the connective tissue caused by mutations in the extracellular matrix protein fibrillin-1, with aortic dissection and aneurysm being its most life-threatening manifestations.
Kidney transplantation for end-stage renal disease (ESRD) in patients with Marfan’s syndrome has not been reported in the literature, and the rate of the incidence of dissection or aneurysm in the iliac artery is unknown.
Here, we present a patient with Marfan’s syndrome with ESRD due to severe renal ischemia caused by massive bleeding from thoracoabdominal aortic dissection leading to transplant surgery of a living kidney procured from the patient’s mother.
After kidney transplantation, the renal function normalized without vascular complications, and stable graft function along with negative results for both microhematuria and proteinuria continued for two years.
Also, vascular complication such as aneurysm or dissection of the iliac artery was not observed using ultrasonography during the follow-up period.
ESRD patients with Marfan’s syndrome might be suitable for kidney transplantation, but long-term and careful observations are needed.
American Psychological Association (APA)
Ryosaka, Makoto& Omoto, Kazuya& Nozaki, Taiji& Yoshida, Kazuhiko& Sawada, Yugo& Hirano, Hajime…[et al.]. 2013. Successful Kidney Transplantation for End-Stage Renal Disease in Marfan's Syndrome. Case Reports in Transplantation،Vol. 2013, no. 2013, pp.1-4.
https://search.emarefa.net/detail/BIM-499851
Modern Language Association (MLA)
Ryosaka, Makoto…[et al.]. Successful Kidney Transplantation for End-Stage Renal Disease in Marfan's Syndrome. Case Reports in Transplantation No. 2013 (2013), pp.1-4.
https://search.emarefa.net/detail/BIM-499851
American Medical Association (AMA)
Ryosaka, Makoto& Omoto, Kazuya& Nozaki, Taiji& Yoshida, Kazuhiko& Sawada, Yugo& Hirano, Hajime…[et al.]. Successful Kidney Transplantation for End-Stage Renal Disease in Marfan's Syndrome. Case Reports in Transplantation. 2013. Vol. 2013, no. 2013, pp.1-4.
https://search.emarefa.net/detail/BIM-499851
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-499851