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Pulmonary Thromboembolism in a Child with Sickle Cell Hemoglobin D Disease in the Setting of Acute Chest Syndrome
Joint Authors
Kuril, Sandeepkumar
Sedrak, Aziza
Villanueva, Hazel
Krajewski, Jennifer
Source
Issue
Vol. 2013, Issue 2013 (31 Dec. 2013), pp.1-3, 3 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2013-09-18
Country of Publication
Egypt
No. of Pages
3
Main Subjects
Abstract EN
Introduction.
Sickle cell hemoglobin D disease (HbSD) is a rare variant of sickle cell disease (SCD).
Incidence of pulmonary thromboembolism (PE) and deep venous thrombosis (DVT) in children with HbSD is unknown.
PE and DVT are known complications of SCD in adults but have not been reported in the literature in children with HbSD.
Case Report.
We are reporting a case of a 12-year-old boy with HbSD with acute chest syndrome (ACS) complicated by complete thrombosis of the branch of the right pulmonary artery and multiple small pulmonary artery emboli seen on computed tomography (CT) pulmonary angiogram and thrombosis of the right brachial vein seen on Doppler ultrasound.
Our patient responded to treatment with anticoagulant therapy.
Conclusion.
There are no cases reported in children with HbSD disease presenting as ACS with pulmonary thromboembolism.
We suggest that PE should be suspected in patients presenting with ACS who do not show improvement with standard management.
CT pulmonary angiogram should be utilized for early diagnosis and appropriate management as there is no current protocol for management of PE/DVT in pediatric patients with SCD.
American Psychological Association (APA)
Villanueva, Hazel& Kuril, Sandeepkumar& Krajewski, Jennifer& Sedrak, Aziza. 2013. Pulmonary Thromboembolism in a Child with Sickle Cell Hemoglobin D Disease in the Setting of Acute Chest Syndrome. Case Reports in Pediatrics،Vol. 2013, no. 2013, pp.1-3.
https://search.emarefa.net/detail/BIM-505408
Modern Language Association (MLA)
Villanueva, Hazel…[et al.]. Pulmonary Thromboembolism in a Child with Sickle Cell Hemoglobin D Disease in the Setting of Acute Chest Syndrome. Case Reports in Pediatrics No. 2013 (2013), pp.1-3.
https://search.emarefa.net/detail/BIM-505408
American Medical Association (AMA)
Villanueva, Hazel& Kuril, Sandeepkumar& Krajewski, Jennifer& Sedrak, Aziza. Pulmonary Thromboembolism in a Child with Sickle Cell Hemoglobin D Disease in the Setting of Acute Chest Syndrome. Case Reports in Pediatrics. 2013. Vol. 2013, no. 2013, pp.1-3.
https://search.emarefa.net/detail/BIM-505408
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-505408