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Cutaneous Epithelioid Clear Cells Angiosarcoma in a Young Woman with Congenital Lymphedema
Joint Authors
de Muret, Anne
de Pinieux, Gonzague
Decouvelaere, Anne-Valérie
Miquelestorena-Standley, Elodie
Tabareau-Delalande, Flore
Source
Issue
Vol. 2013, Issue 2013 (31 Dec. 2013), pp.1-6, 6 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2013-09-03
Country of Publication
Egypt
No. of Pages
6
Main Subjects
Abstract EN
Angiosarcomas are rare aggressive neoplasms that can occur secondary to chronic lymphedema (Stewart-Treves syndrome).
Although secondary angiosarcomas are commonly described after-mastectomy and/or after-radiotherapy, few cases have been reported in association with chronic lymphedema of congenital origin.
We report the clinical, pathological, and cytogenetic findings in a case of cutaneous epithelioid clear cells angiosarcoma that occurred in a 21-year-old woman with hemibody congenital lymphedema.
Surgical biopsies of the tumor mass revealed diffuse epithelioid proliferation of clear atypical cells, for which immunophenotyping highlighted the vascular differentiation.
Despite en bloc resection of the tumor, the patient died of metastatic disease three months after diagnosis.
This case illustrates the clinical and pathology characteristics of angiosarcoma that is a rare entity secondary to chronic lymphedema.
It is the first reported case for which the c-MYC amplification status was assessed.
The diagnostic value of this amplification should be further evaluated in this specific context.
American Psychological Association (APA)
Tabareau-Delalande, Flore& de Muret, Anne& Miquelestorena-Standley, Elodie& Decouvelaere, Anne-Valérie& de Pinieux, Gonzague. 2013. Cutaneous Epithelioid Clear Cells Angiosarcoma in a Young Woman with Congenital Lymphedema. Case Reports in Pathology،Vol. 2013, no. 2013, pp.1-6.
https://search.emarefa.net/detail/BIM-509217
Modern Language Association (MLA)
Tabareau-Delalande, Flore…[et al.]. Cutaneous Epithelioid Clear Cells Angiosarcoma in a Young Woman with Congenital Lymphedema. Case Reports in Pathology No. 2013 (2013), pp.1-6.
https://search.emarefa.net/detail/BIM-509217
American Medical Association (AMA)
Tabareau-Delalande, Flore& de Muret, Anne& Miquelestorena-Standley, Elodie& Decouvelaere, Anne-Valérie& de Pinieux, Gonzague. Cutaneous Epithelioid Clear Cells Angiosarcoma in a Young Woman with Congenital Lymphedema. Case Reports in Pathology. 2013. Vol. 2013, no. 2013, pp.1-6.
https://search.emarefa.net/detail/BIM-509217
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-509217