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Hypersensitivity Vasculitis with Leukocytoclastic Vasculitis Associated with Alpha-1-Proteinase Inhibitor
Joint Authors
Mwirigi, Nicola W.
Thomas, Charles F.
Source
Issue
Vol. 2009, Issue 2009 (31 Dec. 2009), pp.1-6, 6 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2010-02-24
Country of Publication
Egypt
No. of Pages
6
Main Subjects
Abstract EN
Prolastin is a commercially available form of alpha-1-antitrypsin (AAT) that is derived from pooled human plasma and used for treatment of severe alpha-1-antitrypsin deficiency (AATD).
We describe a patient with AATD who developed presumed hypersensitivity vasculitis (HV) following a Prolastin infusion.
Hypersensitivity vasculitis (HV), or cutaneous vasculitis, is characterized by inflammation of the small vessels of the skin with resultant ischemia to the distally supplied areas.
To our knowledge, this is the first reported case of presumed hypersensitivity vasculitis following Prolastin infusion.
American Psychological Association (APA)
Mwirigi, Nicola W.& Thomas, Charles F.. 2010. Hypersensitivity Vasculitis with Leukocytoclastic Vasculitis Associated with Alpha-1-Proteinase Inhibitor. Case Reports in Medicine،Vol. 2009, no. 2009, pp.1-6.
https://search.emarefa.net/detail/BIM-509991
Modern Language Association (MLA)
Mwirigi, Nicola W.& Thomas, Charles F.. Hypersensitivity Vasculitis with Leukocytoclastic Vasculitis Associated with Alpha-1-Proteinase Inhibitor. Case Reports in Medicine No. 2009 (2009), pp.1-6.
https://search.emarefa.net/detail/BIM-509991
American Medical Association (AMA)
Mwirigi, Nicola W.& Thomas, Charles F.. Hypersensitivity Vasculitis with Leukocytoclastic Vasculitis Associated with Alpha-1-Proteinase Inhibitor. Case Reports in Medicine. 2010. Vol. 2009, no. 2009, pp.1-6.
https://search.emarefa.net/detail/BIM-509991
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-509991