Hypersensitivity Vasculitis with Leukocytoclastic Vasculitis Associated with Alpha-1-Proteinase Inhibitor

Joint Authors

Mwirigi, Nicola W.
Thomas, Charles F.

Source

Case Reports in Medicine

Issue

Vol. 2009, Issue 2009 (31 Dec. 2009), pp.1-6, 6 p.

Publisher

Hindawi Publishing Corporation

Publication Date

2010-02-24

Country of Publication

Egypt

No. of Pages

6

Main Subjects

Medicine

Abstract EN

Prolastin is a commercially available form of alpha-1-antitrypsin (AAT) that is derived from pooled human plasma and used for treatment of severe alpha-1-antitrypsin deficiency (AATD).

We describe a patient with AATD who developed presumed hypersensitivity vasculitis (HV) following a Prolastin infusion.

Hypersensitivity vasculitis (HV), or cutaneous vasculitis, is characterized by inflammation of the small vessels of the skin with resultant ischemia to the distally supplied areas.

To our knowledge, this is the first reported case of presumed hypersensitivity vasculitis following Prolastin infusion.

American Psychological Association (APA)

Mwirigi, Nicola W.& Thomas, Charles F.. 2010. Hypersensitivity Vasculitis with Leukocytoclastic Vasculitis Associated with Alpha-1-Proteinase Inhibitor. Case Reports in Medicine،Vol. 2009, no. 2009, pp.1-6.
https://search.emarefa.net/detail/BIM-509991

Modern Language Association (MLA)

Mwirigi, Nicola W.& Thomas, Charles F.. Hypersensitivity Vasculitis with Leukocytoclastic Vasculitis Associated with Alpha-1-Proteinase Inhibitor. Case Reports in Medicine No. 2009 (2009), pp.1-6.
https://search.emarefa.net/detail/BIM-509991

American Medical Association (AMA)

Mwirigi, Nicola W.& Thomas, Charles F.. Hypersensitivity Vasculitis with Leukocytoclastic Vasculitis Associated with Alpha-1-Proteinase Inhibitor. Case Reports in Medicine. 2010. Vol. 2009, no. 2009, pp.1-6.
https://search.emarefa.net/detail/BIM-509991

Data Type

Journal Articles

Language

English

Notes

Includes bibliographical references

Record ID

BIM-509991