Secondary Hemophagocytic Syndrome : The Importance of Clinical Suspicion
Joint Authors
Chacim, Sérgio
Ferreira, Isabel
Domingues, Nelson
Oliveira, Cristina
Mariz, José Mário
Source
Issue
Vol. 2014, Issue 2014 (31 Dec. 2014), pp.1-5, 5 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2014-05-18
Country of Publication
Egypt
No. of Pages
5
Main Subjects
Abstract EN
Hemophagocytic syndrome is a rare and potentially fatal disorder characterized by pathological immune activation associated with a primary familial disorder, genetic mutations, or occurring as a sporadic condition.
The latter can be secondary to infections, malignancies, or autoimmune diseases.
Clinically, patients present signs of severe inflammation, with unremitting fever, cytopenias, spleen enlargement, phagocytosis of bone marrow elements, hypertriglyceridemia, and hypofibrinogenemia.
Increased suspicion is determinant to timely initiate treatment in an attempt to alter the natural history.
The authors present three clinical cases of this syndrome, with a brief review of the diagnostic criteria and treatment.
American Psychological Association (APA)
Oliveira, Cristina& Chacim, Sérgio& Ferreira, Isabel& Domingues, Nelson& Mariz, José Mário. 2014. Secondary Hemophagocytic Syndrome : The Importance of Clinical Suspicion. Case Reports in Hematology،Vol. 2014, no. 2014, pp.1-5.
https://search.emarefa.net/detail/BIM-511442
Modern Language Association (MLA)
Oliveira, Cristina…[et al.]. Secondary Hemophagocytic Syndrome : The Importance of Clinical Suspicion. Case Reports in Hematology No. 2014 (2014), pp.1-5.
https://search.emarefa.net/detail/BIM-511442
American Medical Association (AMA)
Oliveira, Cristina& Chacim, Sérgio& Ferreira, Isabel& Domingues, Nelson& Mariz, José Mário. Secondary Hemophagocytic Syndrome : The Importance of Clinical Suspicion. Case Reports in Hematology. 2014. Vol. 2014, no. 2014, pp.1-5.
https://search.emarefa.net/detail/BIM-511442
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-511442