Renal artery stenosis : an unusual etiology of hypertensive encephalopathy in a child with fanconi anemia
Joint Authors
Purkait, Radheshyam
Mukherji, Aritra
Datta, Sucharita
Bhadra, Ramchandra
Source
Saudi Journal of Kidney Diseases and Transplantation
Issue
Vol. 26, Issue 4 (31 Aug. 2015), pp.778-782, 5 p.
Publisher
Saudi Center for Organ Transplantation
Publication Date
2015-08-31
Country of Publication
Saudi Arabia
No. of Pages
5
Main Subjects
Topics
- Children
- Pulmonary arteries
- Kidneys
- Diseases
- Encephalopathy
- Hypertension
- Diagnosis
- Fanconi’s anemia
- Ascites
- Stenosis
Abstract EN
A 9-year-old girl, diagnosed case of Fanconi anemia, presented with generalized convulsion with altered sensorium.
She had fever, severe pallor, sinus tachycardia, blood pressure of 180/120 mmHg in both upper and lower limb, pan-systolic murmur of grade 2/6, abdominal bruit and bilateral papilledema.
A provisional diagnosis of hypertensive encephalopathy was made and managed with continuous labetalol infusion.
Detailed evaluation including magnetic resonance angiography of renal artery detected underlying atrophic and non-functioning right kidney secondary to severe renal artery stenosis on the same side.
She was started with multiple antihypertensives, but her blood pressure was maintained poorly.
Later on, she underwent rightsided nephrectomy.
Following surgery, she was doing well and maintaining normal blood pressure without any antihypertensives.
Our child is the second reported case of Fanconi anemia associated with renal artery stenosis presenting with hypertensive encephalopathy.
American Psychological Association (APA)
Purkait, Radheshyam& Mukherji, Aritra& Datta, Sucharita& Bhadra, Ramchandra. 2015. Renal artery stenosis : an unusual etiology of hypertensive encephalopathy in a child with fanconi anemia. Saudi Journal of Kidney Diseases and Transplantation،Vol. 26, no. 4, pp.778-782.
https://search.emarefa.net/detail/BIM-592929
Modern Language Association (MLA)
Purkait, Radheshyam…[et al.]. Renal artery stenosis : an unusual etiology of hypertensive encephalopathy in a child with fanconi anemia. Saudi Journal of Kidney Diseases and Transplantation Vol. 26, no. 4 (Jul. / Aug. 2015), pp.778-782.
https://search.emarefa.net/detail/BIM-592929
American Medical Association (AMA)
Purkait, Radheshyam& Mukherji, Aritra& Datta, Sucharita& Bhadra, Ramchandra. Renal artery stenosis : an unusual etiology of hypertensive encephalopathy in a child with fanconi anemia. Saudi Journal of Kidney Diseases and Transplantation. 2015. Vol. 26, no. 4, pp.778-782.
https://search.emarefa.net/detail/BIM-592929
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references : p. 781-782
Record ID
BIM-592929