Management of primitive neuro-ectodermal tumor of the vagina in a sickle cell disease patient

Abstract EN

A twenty-five years old female, a known case of sickle cell disease, presented with frequent and heavy periods of six months duration.

Pelvic ultrasound and MRI showed a vaginal mass pushing the bladder anterioroly; the diagnosis of cervical fibroid was considered.

Histopatholgical examination of the mass revealed a very rare entity of primitive neuroectodermal tumor of the vagina.

This is the first recorded patient of sickle cell disease with primitive neuro-ectodermal tumor of the vagina.

The management was challenging in dealing with her disease and preserving her fertility.