Malignant hepatic perivascular epithelioid cell tumor (PEComa) : case report and a brief review
Joint Authors
Abhirup, Banerjee
Kaushal, Kundalia
Sanket, Mehta
Ganesh, Nagarajan
Source
Journal of the Egyptian National Cancer Institute
Issue
Vol. 27, Issue 4 (31 Dec. 2015), pp.239-242, 4 p.
Publisher
Cairo University National Cancer Institute
Publication Date
2015-12-31
Country of Publication
Egypt
No. of Pages
4
Main Subjects
Topics
Abstract EN
Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal neoplasms which can arise from almost any location in the body.
Diagnosing them pre-operatively is difficult as they mimic features of other hepatic neoplasms including hepatocellular carcinoma (HCC), fibrolamellar HCC, and focal nodular hyperplasia (FNH) among others.
The unique feature of these tumors is the coexpression of muscle and melanocytic markers.
These are identified immunohistochemically by the expression of Human Melanin Black-45 (HMB-45), Melan-A and Smooth Muscle Antigen (SMA) which are seen in the majority of tumors.
The liver is uncommonly associated with a PEComa and the approach to a patient with hepatic PEComa is not well described.
There is no consensus regarding the neo-adjuvant/adjuvant therapy in these patients.
The natural history of this condition is not well documented making it an unpredictable disease.
Here we have discussed a case and reviewed the literature concerning these rare tumors
American Psychological Association (APA)
Abhirup, Banerjee& Kaushal, Kundalia& Sanket, Mehta& Ganesh, Nagarajan. 2015. Malignant hepatic perivascular epithelioid cell tumor (PEComa) : case report and a brief review. Journal of the Egyptian National Cancer Institute،Vol. 27, no. 4, pp.239-242.
https://search.emarefa.net/detail/BIM-648704
Modern Language Association (MLA)
Abhirup, Banerjee…[et al.]. Malignant hepatic perivascular epithelioid cell tumor (PEComa) : case report and a brief review. Journal of the Egyptian National Cancer Institute Vol. 27, no. 4 (Dec. 2015), pp.239-242.
https://search.emarefa.net/detail/BIM-648704
American Medical Association (AMA)
Abhirup, Banerjee& Kaushal, Kundalia& Sanket, Mehta& Ganesh, Nagarajan. Malignant hepatic perivascular epithelioid cell tumor (PEComa) : case report and a brief review. Journal of the Egyptian National Cancer Institute. 2015. Vol. 27, no. 4, pp.239-242.
https://search.emarefa.net/detail/BIM-648704
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references : p. 241-242
Record ID
BIM-648704