Pericardial effusion in langerhans cell histiocytosis : a case report

Abstract EN

Introduction : Langerhans cell histiocytosis (LCH) is a proliferative disorder of histiocytes in multiple organs.

Langerhans cell histiocytosis involves bones, skin, lung and other organs.

Case Presentation : This study describes a seven-month-old Iranian girl who presented with skin rash and cervical lymphadenopathy.

Langerhans cell histiocytosis was suspected when it was associated with anemia, splenomegaly and lytic bone lesions.

A skin biopsy confirmed the diagnosis of Langerhans cell histiocytosis.

During hospitalization, the patient looked ill with respiratory distress.

A chest X-ray showed a ground glass view, and echocardiography showed moderate pericardial effusion.

Conclusions: Pericardial effusion was a rare finding in this case of Langerhans cell histiocytosis.

Pericardial effusion in Langerhans cell histiocytosis, which is an unusual presentation, should be considered when the patient experiences respiratory distress