Case report : a rare cause of complicated urinary tract infection in a woman with Herlyn-Werner-Wunderlich syndrome

Abstract EN

Introduction : Urinary tract infection is a common disease in the general population.

However, in patients with frequent urinary tract infection, it is important to determine any treatable cause to avoid recurrence.

Case Presentation : Herlyn-Werner-Wunderlich syndrome or OHVIRA syndrome is a very rare congenital anomaly with uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis.

The earliest presentation of this syndrome is hematocolpos that develops during menstruation and results in dysmenorrhea and a pelvic mass shortly after menarche.

Herein, we report a patient with Herlyn-Werner-Wunderlich syndrome manifested with unusual symptoms, delayed onset and without surgery.

The unique point of this patient is the partial obstruction of cervico-vaginal junction.

Conclusions : Early diagnosis and timely treatment of OHVIRA syndrome can prevent long-term complications, such as recurrent urinary tract infection and infertility.

A high index of suspicion is required, even though OHVIRA syndrome is extremely rare and may have an atypical presentation.